Amyloidogenesis-associated Polyneuropathy

Amyloid deposits around nerves can damage and disrupt smooth information processing between the brain and organs. Here is the latest research on amyloidosis-associated polyneuropathies.

December 29, 2020

Early changes of nerve integrity in preclinical carriers of hereditary transthyretin Ala117Ser amyloidosis with polyneuropathy

European Journal of Neurology : the Official Journal of the European Federation of Neurological Societies
Ming-Chang ChiangSung-Tsang Hsieh
September 15, 2020
Open Access

Clinical and genetic features of transthyretin-related familial amyloid polyneuropathy in China

Chinese Medical Journal
Lei LiuRu-Xu Zhang
October 2, 2020
Open Access

Repurposing Benzbromarone for Familial Amyloid Polyneuropathy: A New Transthyretin Tetramer Stabilizer

International Journal of Molecular Sciences
Ellen Y CotrinaGemma Arsequell
December 18, 2020
Open Access

Clinical 3-D Gait Assessment of Patients With Polyneuropathy Associated With Hereditary Transthyretin Amyloidosis

Frontiers in Neurology
Maria do Carmo Vilas-BoasJoão Paulo Silva Cunha
October 13, 2020

Advances in pharmacotherapy for cardiac amyloidosis

Expert Opinion on Pharmacotherapy
R SpoladoreG Fragasso
October 5, 2020
Case Report
Open Access

Isolated atrial amyloidosis suspected by electrophysiological voltage mapping and diagnosed by 99m Tc-DPD scintigraphy

ESC Heart Failure
Schöppenthau DoreenMessroghli Daniel
December 18, 2020
Case Report
Open Access

Domino living donor liver transplantation of familial amyloid polyneuropathy patient - A case report

Anesthesia and Pain Medicine
Sungrok ChaGaab Soo Kim
December 8, 2020
Open Access

Ligand conjugated antisense oligonucleotide for the treatment of transthyretin amyloidosis: preclinical and phase 1 data

ESC Heart Failure
Nicholas J VineyBrett P Monia
November 13, 2020
Open Access

Association of the Transthyretin Variant V122I With Polyneuropathy Among Individuals of African Descent

MedRxiv : the Preprint Server for Health Sciences
M. M. ParkerPaul Nioi
December 8, 2020
Open Access

Real-world outcomes in non-endemic hereditary transthyretin amyloidosis with polyneuropathy: a 20-year German single-referral centre experience

Amyloid : the International Journal of Experimental and Clinical Investigation : the Official Journal of the International Society of Amyloidosis
Matthias N UngererMarkus Weiler
October 30, 2020
Open Access

hATTR Pathology: Nerve Biopsy Results from Italian Referral Centers

Brain Sciences
Marco LuigettiMario Sabatelli
September 9, 2020
Open Access

Red flags in patients with hereditary transthyretin amyloidosis at diagnosis in a non-endemic area of Spain

Neurología : publicación oficial de la Sociedad Española de Neurología
L Silva-HernándezL Galán Dávila
October 1, 2020

Differential involvement of myelinated and unmyelinated nerve fibers in painful diabetic polyneuropathy

Muscle & Nerve
Eleonora GalosiAndrea Truini
January 8, 2021
Open Access

Religious affiliation and COVID-19-related mortality: a retrospective cohort study of prelockdown and postlockdown risks in England and Wales

Journal of Epidemiology and Community Health
Charlotte Hannah GaughanNeil Bannister
December 16, 2020
Open Access

Advances in Treatment of ATTRv Amyloidosis: State of the Art and Future Prospects

Brain Sciences
Massimo RussoAnna Mazzeo
September 17, 2020

Nerve ultrasonography findings as possible pitfall in differential diagnosis between hereditary transthyretin amyloidosis with polyneuropathy and chronic inflammatory demyelinating polyneuropathy

Neurological Sciences : Official Journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
Luca LeonardiGiovanni Antonini

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