Creutzfeldt-Jakob Disease

Creutzfeldt-Jakob Disease is a fatal neurodegenerative disease caused by aggregation and accumulation of misfolded prion proteins. Here are the latest discoveries pertaining to this disease.

April 12, 2021

Non-white cases of sporadic Creutzfeldt-Jakob disease: A 28 year review of United Kingdom National Surveillance Data.

Journal of the Neurological Sciences
Gavin LanglandsSuvankar Pal
April 10, 2021
Preprint
Open Access

Variant Creutzfeldt-Jakob Disease: The Challenge of Preventing a Rare but Potentially Devastating Exposure

MedRxiv : the Preprint Server for Health Sciences
R. PandeyEmil Lesho
April 4, 2021
Open Access

Vaporized Hydrogen Peroxide and Ozone Gas Synergistically Reduce Prion Infectivity on Stainless Steel Wire.

International Journal of Molecular Sciences
Hideyuki HaraSuehiro Sakaguchi
April 3, 2021
Open Access

Oral administration of repurposed drug targeting Cyp46A1 increases survival times of prion infected mice.

Acta Neuropathologica Communications
Tahir AliSabine Gilch
March 31, 2021
Case Report

Sporadic Creutzfeldt-Jacob disease presenting as epilepsia partialis continua and non-ictal nystagmus.

European Journal of Neurology : the Official Journal of the European Federation of Neurological Societies
Inês Antunes CunhaConceição Bento
March 31, 2021

Early and long-term cognitive features in sporadic Creutzfeldt-Jakob disease.

Neurological Sciences : Official Journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
M MeattiniA R Giovagnoli
March 31, 2021

Spatial distribution of abnormal EEG activity in Creutzfeldt-Jakob disease.

Neurophysiologie clinique = Clinical neurophysiology
Shmuel AppelIlan Blatt
March 27, 2021
Open Access

Distribution of microRNA profiles in pre-clinical and clinical forms of murine and human prion disease.

Communications Biology
Lesley ChengAndrew F Hill
March 27, 2021
Open Access

Two distinct conformers of PrPD type 1 of sporadic Creutzfeldt-Jakob disease with codon 129VV genotype faithfully propagate in vivo.

Acta Neuropathologica Communications
Ignazio CaliPierluigi Gambetti
March 26, 2021
Preprint
Open Access

Diagnostic accuracy of cerebrospinal fluid and blood biomarkers for the differential diagnosis of sporadic Creutzfeldt-Jakob disease: a (network) meta-analysis

MedRxiv : the Preprint Server for Health Sciences
N. RübsamenA. Karch
March 26, 2021

[Creutzfeldt-Jakob Disease].

No shinkei geka. Neurological surgery
Aki Sato
March 18, 2021
Review
Open Access

Creutzfeldt-Jakob and Vascular Brain Diseases: Their Overlap and Relationships.

Frontiers in Neurology
Yacov BalashRonit Gilad
March 18, 2021
Open Access

Human cerebral organoids as a therapeutic drug screening model for Creutzfeldt-Jakob disease.

Scientific Reports
Bradley R GrovemanCathryn L Haigh
March 11, 2021
Comment / Editorial

Diagnostic Value of Electroencephalogram in Creutzfeldt-Jakob Disease.

Annals of Indian Academy of Neurology
Kurupath Radhakrishnan
March 11, 2021

EEG Observations in Probable Sporadic CJD.

Annals of Indian Academy of Neurology
Ravindranadh Chowdary MundlamurriSanjib Sinha

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