Gerstmann-Straussler-Scheinker Disease

Gerstmann-Straussler-Scheinker disease is a rare neurodegenerative disorder caused by prions and characterized by symptoms associated with prion-associated diseases. Here is the latest research.

June 20, 2020

Evidence Linking Protein Misfolding to Quality Control in Progressive Neurodegenerative Diseases

Current Topics in Medicinal Chemistry
Md Tanvir KabirMohamed M Abdel-Daim
June 21, 2020
Open Access

An astrocyte cell line that differentially propagates murine prions

The Journal of Biological Chemistry
Waqas TahirHermann M Schätzl
June 27, 2020
Case Report
Open Access

Intrafamilial phenotypic variation in spinocerebellar ataxia type 23

Cerebellum & Ataxias
Shunichi SatohKunihiro Yoshida
June 24, 2020

Diagnosis of Prion Diseases by RT-QuIC Results in Improved Surveillance

Neurology
Daniel D RhoadsBrian S Appleby
June 23, 2020
Review

Genetic risk factors for Creutzfeldt-Jakob disease

Neurobiology of Disease
Emma Jones, Simon Mead
July 7, 2020
Preprint
Open Access

Dimeric prion protein ligand activates Adgrg6 but does not rescue myelinopathy of PrP-deficient mice

BioRxiv : the Preprint Server for Biology
A. HenziAdriano Aguzzi
June 21, 2020

Application of yeast to studying amyloid and prion diseases

Advances in Genetics
Yury O ChernoffTatiana A Chernova
July 7, 2020
Open Access

Insects in food and feed - allergenicity risk assessment and analytical detection

EFSA Journal
German Federal Institute for Risk Assessment (BfR), National Reference Laboratory for Animal protein in Feed, NRL‐APAlbert Braeuning
July 8, 2020
Open Access

Recent developments in antibody therapeutics against prion disease

Emerging Topics in Life Sciences
Karl Frontzek, Adriano Aguzzi
July 3, 2020
Preprint
Open Access

Cerebellar degeneration reduces memory resilience after extended training

BioRxiv : the Preprint Server for Biology
Thomas HulstO. Donchin
July 9, 2020
Open Access

A novel PRNP -G131R variant associated with familial prion disease

Neurology. Genetics
Jumana T AlshaikhJames A Mastrianni
July 7, 2020

Copper and iron ions accelerate the prion-like propagation of α-synuclein: A vicious cycle in Parkinson's disease

International Journal of Biological Macromolecules
Yang LiKun Huang

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