Gerstmann-Straussler-Scheinker Disease

Gerstmann-Straussler-Scheinker disease is a rare neurodegenerative disorder caused by prions and characterized by symptoms similar to other prion-associated diseases. Here is the latest research.

December 29, 2021
Open Access

Differential Accumulation of Misfolded Prion Strains in Natural Hosts of Prion Diseases.

Zoe J LambertM Heather West Greenlee
June 21, 2021

[Prion diseases or transmissible spongiform encephalopathies].

La Revue de médecine interne
J-P Brandel
December 17, 2020
Open Access

Structural Features of Heparin and Its Interactions With Cellular Prion Protein Measured by Surface Plasmon Resonance.

Frontiers in Molecular Biosciences
So Young KimRobert J Linhardt
January 1, 2020
Case Report
Open Access

A case of Gerstmann-Straussler-Scheinker (GSS) disease with supranuclear gaze palsy

Journal of Clinical Movement Disorders
Nicole A UfkesMarian L Dale
September 19, 2019

Prion Disease

Seminars in Neurology
Kelly J Baldwin, Cynthia M Correll
July 25, 2018
Open Access

Human prion diseases: current issues

Zhurnal nevrologii i psikhiatrii imeni S.S. Korsakova
N N ZavadenkoE N Saverskaya
January 20, 2018

In Situ Tissue Labeling of Cerebral Amyloid Using HIV-Related Tat Peptide

Molecular Neurobiology
E MadernaG Giaccone
November 18, 2017
Case Report

Gerstmann-Straussler-Scheinker disease with PRNP P102L heterozygous mutation presenting as progressive myoclonus epilepsy

European Journal of Neurology : the Official Journal of the European Federation of Neurological Societies
L MumoliA Gambardella
September 2, 2017
Open Access

Purification and Fibrillation of Full-Length Recombinant PrP

Methods in Molecular Biology
Natallia MakaravaIlia V Baskakov
April 19, 2017
Open Access

A family with hereditary cerebellar ataxia finally confirmed as Gerstmann-Straussler-Scheinker syndrome with P102L mutation in PRNP gene

Neurosciences : the Official Journal of the Pan Arab Union of Neurological Sciences
Ling LongZhengqi Lu
January 23, 2017

Neuroradiology of human prion diseases, diagnosis and differential diagnosis

La Radiologia medica
Simona GaudinoCesare Colosimo
November 5, 2016

Oxidative stress and mitochondrial dysfunction-linked neurodegenerative disorders

Neurological Research
Md Torequl Islam
May 20, 2016
Open Access

Prions in dentistry: A need to be concerned and known

Journal of Oral and Maxillofacial Pathology : JOMFP
B SushmaShambhvi A Malik
July 16, 2015
Open Access

Prion Protein Prolines 102 and 105 and the Surrounding Lysine Cluster Impede Amyloid Formation.

The Journal of Biological Chemistry
Allison KrausByron Caughey

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