Hereditary Demyelinating Diseases of the CNS

Hereditary demyelinating diseases of the central nervous systems are caused primarily due to inherited genetic conditions. Examples include Alexander, Canavan, and Pelizaeus-Merzbacher diseases. Here is the latest research.

December 30, 2020
Review
Open Access

Evolution of Adrenoleukodystrophy Model Systems

Journal of Inherited Metabolic Disease
Roberto MontoroMarc Engelen
January 14, 2021
Review
Open Access

Mitochondrial dysfunction in nonalcoholic fatty liver disease and alcohol related liver disease

Translational Gastroenterology and Hepatology
Pankaj PrasunKimihiko Oishi
December 29, 2020

Interleukin-6 inhibition with tocilizumab for relapsing MOG-IgG associated disorder (MOGAD): A case-series and review

Multiple Sclerosis and Related Disorders
Paul M ElsberndDean M Wingerchuk
January 15, 2021
Preprint
Open Access

Renal Denervation Ameliorates Cardiomyocyte Apoptosis in Myocardial Ischemia-reperfusion Injury

ResearchSquare
Zheng ZhaoYiyao Jiang
December 18, 2020

Lipid alterations in human frontal cortex in ALS-FTLD-TDP43 proteinopathy spectrum are partly related to peroxisome impairment

Neuropathology and Applied Neurobiology
Pol Andrés-BenitoIsidro Ferrer
December 29, 2020
Open Access

Whitening effect of novel peptide mixture by regulating melanosome biogenesis, transfer and degradation

The Korean Journal of Physiology & Pharmacology : Official Journal of the Korean Physiological Society and the Korean Society of Pharmacology
Eung-Ji LeeEun Mi Kim
December 15, 2020

Clinical evaluation of childhood cerebral adrenoleukodystrophy with balint's symptoms

Brain & Development
Kazuo KubotaNobuyuki Shimozawa
January 17, 2021

Alcoholic liver disease and autoimmune hepatitis: Sometimes a closer look under the surface is needed

European Journal of Internal Medicine
Eirini I RigopoulouGeorge N Dalekos
January 15, 2021

GRK2 mediates β-arrestin interactions with 5-HT2 receptors for JC polyomavirus endocytosis

Journal of Virology
Colleen L MayberryMelissa S Maginnis
January 9, 2021

Peroxisomal Dysfunction and Oxidative Stress in Neurodegenerative Disease: A Bidirectional Crosstalk

Advances in Experimental Medicine and Biology
Marc FransenPaul P Van Veldhoven
January 5, 2021
Open Access

Targeted Metabolomics Identifies Differential Serum and Liver Amino Acids Biomarkers in Rats with Alcoholic Liver Disease

Journal of Nutritional Science and Vitaminology
Chenze ShiTao Wu
January 7, 2021
Case Report
Open Access

The Role of Non-Selective TNF Inhibitors in Demyelinating Events

Brain Sciences
Line Buch KristensenHelle H Nielsen

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