A case of Behçet's disease with pericarditis, thrombotic thrombocytopenic purpura, deep vein thrombosis and coronary artery pseudo aneurysm.

The Korean Journal of Internal Medicine
Chang Mo KwonChoong Ki Lee

Abstract

Behçet's disease with concomitant thrombotic thrombocytopenic purpura (TTP), coronary artery stenosis and coronary artery pseudo aneurysm is rare. Here we report a case of Behçet's disease with several cardiovascular complications, namely: pericarditis, deep vein thrombosis (DVT), TTP, coronary artery stenosis, and a coronary artery pseudo aneurysm. A 37-year-old female presented with sudden dyspnea and syncope at our emergency room and underwent pericardiectomy and pericardial window formation for the diagnosis of cardiac tamponade with acute hemorrhagic pericarditis. Thereafter, TTP and DVT complicated her illness. After confirmation of Behçet's disease on the basis of a history of recurrent oral and genital ulcers and erythema nodosum, remission was achieved after treatment with methylprednisolone pulse therapy, colchicine, catheter directed thrombolysis and thrombectomy. However, whilst maintaining anticoagulation therapy, a newly developed pericardial aneurysmal dilatation was noted on follow-up radiologic evaluation. Further evaluation revealed right coronary artery stenosis and a left coronary artery pseudo aneurysm; these additional problems were treated with the nonsurgical insertion of an endovascular graft stent. At ...Continue Reading

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Citations

Oct 16, 2009·Clinical Rheumatology·Yusuf SezenRamazan Geyik
Jan 3, 2014·International Journal of Rheumatic Diseases·Ramyah RajakulasingamCharis Costopoulos
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Feb 20, 2021·Journal of Experimental Pharmacology·Burçin Cansu Bozca, Erkan Alpsoy

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Methods Mentioned

BETA
X-ray
ESR
coronary artery bypass

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