A cross-sectional nationwide survey on esophageal atresia and tracheoesophageal fistula

Journal of Pediatric Surgery
A Pini PratoM Nobili

Abstract

Our study aims at disclosing epidemiology and most relevant clinical features of esophageal atresia (EA) pointing to a model of multicentre collaboration. A detailed questionnaire was sent to all Italian Units of pediatric surgery in order to collect data of patients born with EA between January and December 2012. The results were crosschecked by matching date and place of birth of the patients with those of diagnosis-related group provided by the Italian Ministry of Health (MOH). A total of 146 questionnaires were returned plus a further 32 patients reported in the MOH database. Basing on a total of 178 patients with EA born in Italy in 2012, the incidence of EA was calculated in 3.33 per 10,000 live births. Antenatal diagnosis was suspected in 29.5% patients. 55.5% showed associated anomalies. The most common type of EA was Gross type C (89%). Postoperative complications occurred in 37% of type C EA and 100% of type A EA. A 9.5% mortality rate was reported. This is the first Italian cross-sectional nationwide survey on EA. We can now develop shared guidelines and provide more reliable prognostic expectations for our patients.

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Citations

Mar 5, 2016·Birth Defects Research. Part A, Clinical and Molecular Teratology·Matteo CassinaMaurizio Clementi
Sep 22, 2015·Journal of Pediatric Surgery·Haitao ZhuShan Zheng
Apr 27, 2016·Journal of Pediatric Surgery·Felipe DonosoHelene Engstrand Lilja
Sep 28, 2017·International Journal of Environmental Research and Public Health·Maria Francesca PatriaSusanna Esposito
May 9, 2018·Journal of Pediatric Gastroenterology and Nutrition·Michaela Dellenmark-BlomKate Abrahamsson
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Sep 20, 2019·Pediatric Pulmonology·Felipe DonosoHelene E Lilja
Dec 5, 2017·Surgery Research and Practice·Julia EkseliusPernilla Stenström
Jul 11, 2020·European Journal of Pediatrics·Yi-Hsuan LuHung-Chieh Chou
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Dec 8, 2020·Frontiers in Pediatrics·Laura Antonia RitzJochen Hubertus
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Nov 19, 2020·Arquivos Brasileiros De Cirurgia Digestiva : ABCD = Brazilian Archives of Digestive Surgery·Shahnam AskarpourMohsen Ali-Samir

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