PMID: 9434026Jan 20, 1998Paper

A peculiar form of multiple cystic dilatation of the intrahepatic biliary system found in a patient with biliary atresia

Journal of Pediatric Surgery
A TakahashiS Matsuyama

Abstract

The authors report a peculiar form of intrahepatic multiple cysts of the biliary system in a patient with biliary atresia (BA). An 11-year-old girl was admitted to our institution to be investigated for repeated cholangitis occurring after the age of 10 years. She underwent a hepaticojejunostomy, caused by Type I (cyst-type) BA, in the neonatal period. The radiological examination results showed multiple cystic dilatation of the intrahepatic biliary system with a vascular structure protruding into the cyst lumen. Such cystic dilatation with a protruding vascular structure has been noted in patients with Caroli's disease and congenital hepatic fibrosis, and ductal plate malformation is shown to be responsible for the cyst formation. The authors postulate that such malformation of the intrahepatic biliary system is related to the cyst formation in our case.

References

Feb 1, 1986·Radiology·G J MarchalA L Baert
Aug 1, 1985·Journal of Pediatric Gastroenterology and Nutrition·S L WerlinR Nathan
Jan 1, 1985·Journal of Hepatology·V J Desmet

❮ Previous
Next ❯

Citations

Jul 27, 1999·Hepatology : Official Journal of the American Association for the Study of Liver Diseases·M V MazziottiD H Perlmutter
Dec 21, 2007·Pediatric Surgery International·Takahisa TainakaHisami Ando
May 23, 2008·Journal of Clinical Gastroenterology·Mikelle D Bassett, Karen F Murray
Jul 5, 2015·Pediatric Surgery International·Mohamed SafwanMohamed Rela
Jan 6, 2007·Journal of Pediatric Gastroenterology and Nutrition·Takahisa TainakaHisami Ando
Jun 11, 2020·Future Science OA·Mukul Vij, Mohamed Rela

❮ Previous
Next ❯

Related Concepts

Related Feeds

Carcinoma, Ductal

Ductal carcinoma is a malignant neoplasm involving the ductal systems of any of a number of organs, such as the mammary glands, pancreas, prostate or lacrimal gland. Discover the latest research on ductal carcinoma here.