Abnormalities of intestinal rotation in patients with congenital heart disease and the heterotaxy syndrome

Congenital Heart Disease
Barbara FerdmanJ Rychik

Abstract

Abnormalities of intestinal rotation (AIR) are seen in association with congenital heart disease and heterotaxy syndrome. The prevalence of these abnormalities and recommendations for management are unclear. Our objective was to determine the prevalence of screening for AIR by elective imaging among our group and prophylactic vs. emergent surgical intervention for AIR in patients with congenital heart disease and heterotaxy syndrome. From October 1988 through October 2000, we identified 74 patients with congenital heart disease and heterotaxy syndrome, 44 (59%) asplenia, 30 (41%) polysplenia. Abdominal imaging was performed in 34 patients (45%). Twenty-four (32%) were found to have AIR. Of 34 patients imaged, 22 (65%) were found to have AIR. Two patients not imaged were found to have AIR: one at autopsy, and the other, incidentally during other abdominal surgery. Because imaging was performed based on individual cardiologist's practice style that did not change over the period of the study and rarely secondary to symptoms, it is likely that the prevalence of AIR in the patients that were not electively imaged would be similar. There was no statistical difference in the presence of AIR between asplenic (34%[15/44]) and polysplen...Continue Reading

References

Jan 1, 1990·Clinical and Laboratory Haematology·G R CorazzaD Quaglino
Nov 1, 1989·Archives of Disease in Childhood·M R SharlandD P Drake
Aug 1, 1989·Journal of Pediatric Surgery·D M PowellC D Smith
Apr 1, 1983·Pediatric Cardiology·W M PeoplesJ E Edwards
Jan 1, 1982·Pediatric Cardiology·W BermanT Dillon
Oct 1, 1982·Journal of Pediatric Surgery·R J Paddock, R M Arensman
Aug 1, 1981·Journal of Pediatric Surgery·H C Filston, D R Kirks
Mar 1, 1995·Journal of Pediatric Surgery·J VazquezJ A Tovar
May 1, 1993·World Journal of Surgery·A M Torres, M M Ziegler
Jan 1, 1993·Journal of Pediatric Surgery·W L ScheyJ R Sty
Jan 1, 1997·Journal of Pediatric Surgery·K NakadaN Yamate
May 7, 1998·Pediatric Radiology·M R Ditchfield, J M Hutson
Feb 27, 1999·The Journal of Thoracic and Cardiovascular Surgery·J William GaynorT L Spray
Aug 28, 1999·Radiographics : a Review Publication of the Radiological Society of North America, Inc·Kimberly E ApplegateD Murphy
Feb 9, 2000·Pediatric Surgery International·A V DilleyG M Henry
Mar 21, 2001·Genetics in Medicine : Official Journal of the American College of Medical Genetics·A E LinL B Holmes
May 29, 2001·American Journal of Medical Genetics·I S Kathiriya, D Srivastava
Nov 13, 2004·Pediatric Radiology·Jeremy AidlenDaniel P Doody

Citations

Feb 23, 2008·Cardiology in the Young·Meryl S CohenPaul M Weinberg
Apr 17, 2014·Pediatric and Developmental Pathology : the Official Journal of the Society for Pediatric Pathology and the Paediatric Pathology Society·Elizabeth C BurtonLisa Rooper
Dec 10, 2014·Journal of Pediatric Surgery·Craig T ElderEric Scaife
Feb 13, 2016·Cardiovascular Pathology : the Official Journal of the Society for Cardiovascular Pathology·Rohit S LoombaRobert H Anderson
Apr 28, 2010·Journal of Cardiothoracic and Vascular Anesthesia·Glyn D Williams, Angela Feng
Jun 9, 2009·Pediatric Clinics of North America·Emily F Durkin, Aimen Shaaban
Jun 26, 2013·Pediatric Cardiology·Venugopal AmulaMadolin K Witte
Sep 29, 2015·Journal of Pediatric Surgery·Paul S CullisPaul D Losty
Mar 19, 2015·Journal of Pediatric Surgery·Arash SalavitabarWyman W Lai
Jun 6, 2009·Congenital Anomalies·Satoko KatsuyaIkuo Konishi
Jan 18, 2015·The Annals of Thoracic Surgery·Shawndip SenGanga Krishnamurthy
Apr 19, 2015·Current Opinion in Pediatrics·Daniel L LodwickKatherine J Deans
Dec 26, 2017·Texas Heart Institute Journal·Safieh GolestanehTimothy G Egan
Oct 30, 2018·Radiologia brasileira·Lucas Samuel Perinazzo PauvelsCarlos Jesus Pereira Haygert
Nov 16, 2016·Current Treatment Options in Cardiovascular Medicine·Karl Degenhardt, J Rychik
May 31, 2021·The American Journal of the Medical Sciences·Muhammad SoofiVaskar Mukerji

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