Acquired Chiari-I malformation and hydromyelia secondary to a giant craniopharyngioma

Pediatric Neurosurgery
M LeeJ H Wisoff

Abstract

Hydromyelia, or hydrosyringomyelia is frequently associated with the Chiari I malformation of the cerebellar tonsils. Descent of the cerebellar tonsils is considered a congenital anomaly with a few reports of 'acquired' Chiari I malformation. We report a patient with a giant craniopharyngioma and hydrocephalus who at presentation had a concomitant Chiari I malformation and hydromyelia. The patient underwent gross total resection of the tumor and, with no further treatment, demonstrated spontaneous resolution of the Chiari I malformation and hydromyelia during the postoperative period. This suggests that the Chiari I malformation and the resulting hydromyelia were 'acquired', and were caused by an intracranial mass effect. This provides further evidence for an associative mechanism of cerebellar tonsillar descent and the development of hydromyelia.

Citations

Feb 25, 2009·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·Dharmendra GanesanDominic N Thompson
Mar 3, 2007·Journal of Neurosurgery·Taylor J AbelAnthony M Avellino
Aug 8, 2009·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·Yassine El HassaniBenedict Rilliet
Sep 20, 2011·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·Concezio Di RoccoSimone Peraio
Oct 1, 2005·Pediatric Neurosurgery·Abderrahmane HamlatBeatrice Carsin-Nicol
Jun 23, 2019·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·Luca MassimiMassimo Caldarelli

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