PMID: 9551464Apr 29, 1998Paper

Acute intermittent porphyria with transient paresis and contracture. Evidence for initial myopathic dysfunction?

Der Nervenarzt
M Poersch

Abstract

A 70-year old man with acute intermittent porphyria had acute transient bibrachial paresis with moderate contracture of the involved muscles, which showed electrical silence in a conventional electromyographic investigation with surface electrodes placed over the contracted muscle belly (filter: 20 Hz-2 Hz, amplifier 50 microV). Slow finger movements were still possible and showed typical muscle-action potentials. This electroclinical correlation points to myopathic localized dysfunction, perhaps similar to rare case reports with patients having metabolic myopathy of McArdle's type.

Citations

Oct 21, 2016·Acta Neurologica Scandinavica·J FinstererW Grisold

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