Adenomas in glycogen storage disease type 1. Two cases with unusual histologic features

The American Journal of Surgical Pathology
R Poe, D C Snover


Two cases of hepatic adenomas arising in patients with glycogen storage disease type I are presented. In both cases, the adenomas showed unusual histological features including marked fatty change, a polymorphonuclear infiltrate, Mallory hyalin, and lamellar fibrosis. In addition, one case was associated with amyloidosis. Such features have only recently been described in adenomas and have not been reported previously in association with glycogen storage disease type I.


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Related Concepts

Cytoplasmic Inclusion (Cell Structure)
Glycogen Storage Disease Type I
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Peroxidase-Antiperoxidase Complex Technique
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Electron Microscopy

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