PMID: 2098249Dec 1, 1990Paper

Adrenomyeloneuropathy in 4 brothers

Zhonghua shen jing jing shen ke za zhi = Chinese journal of neurology and psychiatry
X Zhao

Abstract

Four brothers with adrenomyeloneuropathy are reported. They have developed darkening of the skin the sign of adrenal insufficiency at age of 5-10. During 10 years after that time progressive spastic paraparesis has appeared gradually in all of them and has had aggrevative tendency abruptly in late. Three male cousins of the proband probably died of "juvenile type" of adrenoleucodystrophy.

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