PMID: 8586141Oct 1, 1995Paper

An adult case of lymphangiomatosis of the mediastinum, pulmonary interstitium and retroperitoneum complicated by chronic disseminated intravascular coagulation

The European Respiratory Journal
K TakahashiS Kira

Abstract

Pulmonary lymphangiomatosis is a rare clinical and pathological entity which is distinct from lymphangiomyomatosis and from pulmonary lymphangiectasis. We report a case of a 20 year old man with diffuse lymphangiomatosis involving the mediastinum, lungs and retroperitoneum. The patient's intrathoracic lymphangiomatosis produced restrictive and obstructive impairment of his pulmonary function, but did not result in chylothorax or chylopericardium, which are two common manifestations of the disease. The patient's clinical course was remarkable for the concomitant development of chronic disseminated intravascular coagulation (DIC). Lymphangiomatosis involving both the mediastinum and pulmonary parenchyma is rare, and DIC is a very unusual complication of lymphangiomatosis.

Citations

Feb 10, 2004·Journal of Pediatric Hematology/oncology·Ofelia A AlvarezCraig W Zuppan
Dec 14, 2005·Journal of Pediatric Hematology/oncology·Zeynep TamayFeryal Gun
Mar 11, 2000·American Journal of Respiratory and Critical Care Medicine·J L FaulT A Raffin
Sep 15, 2006·Mayo Clinic Proceedings·John G ParkDavid E Midthun
Feb 13, 2017·Experimental and Molecular Pathology·Addie B SpierDavid Sears
Mar 21, 2008·Seminars in Diagnostic Pathology·Sachiv ShethMichael C Fishbein
May 23, 2003·Anesthesia and Analgesia·Isuta NishioJules H Sumkin
Nov 23, 2006·Virchows Archiv : an International Journal of Pathology·Jun-ichiro IkedaKatsuyuki Aozasa
Nov 19, 2009·Wiener klinische Wochenschrift·Ina SteinacherMichael Studnicka
Jun 2, 2016·European Respiratory Review : an Official Journal of the European Respiratory Society·Francesca LuisiSergio Harari
Oct 17, 2014·American Journal of Clinical Pathology·Stefano LicciStefano Ascani
Nov 8, 2016·Journal of Pediatric Hematology/oncology·Anirban DasAshim Das
Aug 29, 2007·Jornal brasileiro de pneumologia : publicaça̋o oficial da Sociedade Brasileira de Pneumologia e Tisilogia·Adma Silva de LimaDante Luis Escuissato
Feb 5, 1999·Annals of Oncology : Official Journal of the European Society for Medical Oncology·J Andrade SantiagoF Lobo

❮ Previous
Next ❯

Related Concepts

Trending Feeds

COVID-19

Coronaviruses encompass a large family of viruses that cause the common cold as well as more serious diseases, such as the ongoing outbreak of coronavirus disease 2019 (COVID-19; formally known as 2019-nCoV). Coronaviruses can spread from animals to humans; symptoms include fever, cough, shortness of breath, and breathing difficulties; in more severe cases, infection can lead to death. This feed covers recent research on COVID-19.

Blastomycosis

Blastomycosis fungal infections spread through inhaling Blastomyces dermatitidis spores. Discover the latest research on blastomycosis fungal infections here.

Nuclear Pore Complex in ALS/FTD

Alterations in nucleocytoplasmic transport, controlled by the nuclear pore complex, may be involved in the pathomechanism underlying multiple neurodegenerative diseases including Amyotrophic Lateral Sclerosis and Frontotemporal Dementia. Here is the latest research on the nuclear pore complex in ALS and FTD.

Applications of Molecular Barcoding

The concept of molecular barcoding is that each original DNA or RNA molecule is attached to a unique sequence barcode. Sequence reads having different barcodes represent different original molecules, while sequence reads having the same barcode are results of PCR duplication from one original molecule. Discover the latest research on molecular barcoding here.

Chronic Fatigue Syndrome

Chronic fatigue syndrome is a disease characterized by unexplained disabling fatigue; the pathology of which is incompletely understood. Discover the latest research on chronic fatigue syndrome here.

Evolution of Pluripotency

Pluripotency refers to the ability of a cell to develop into three primary germ cell layers of the embryo. This feed focuses on the mechanisms that underlie the evolution of pluripotency. Here is the latest research.

Position Effect Variegation

Position Effect Variagation occurs when a gene is inactivated due to its positioning near heterochromatic regions within a chromosome. Discover the latest research on Position Effect Variagation here.

STING Receptor Agonists

Stimulator of IFN genes (STING) are a group of transmembrane proteins that are involved in the induction of type I interferon that is important in the innate immune response. The stimulation of STING has been an active area of research in the treatment of cancer and infectious diseases. Here is the latest research on STING receptor agonists.

Microbicide

Microbicides are products that can be applied to vaginal or rectal mucosal surfaces with the goal of preventing, or at least significantly reducing, the transmission of sexually transmitted infections. Here is the latest research on microbicides.