An unusual form of supracardiac total anomalous pulmonary venous return via a right-sided vertical vein in a heterotaxy syndrome case.

Pediatric Cardiology
Anja LehnerKatarzyna Januszewska

Abstract

Heterotaxy syndromes comprise a great variety of possible cardiac defects. Anomalies of the pulmonary venous system are well recognized in heterotaxy syndromes but constitute a frequently underdiagnosed subgroup. The case report describes a girl with a rare form of supracardiac total anomalous pulmonary venous return via a right-sided vertical vein to the right innominate vein in heterotaxy syndrome with dextrocardia, unbalanced atrioventricular septal defect with severe left ventricular hypoplasia, and transposition of the great arteries with pulmonary stenosis. Careful evaluation and imaging before surgical repair is crucial for such complex cardiac anomalies.

References

Apr 30, 1998·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·V E BrownG S Shirali
Sep 30, 2005·Developmental Dynamics : an Official Publication of the American Association of Anatomists·Robert H AndersonAntoon F M Moorman
May 11, 2010·European Journal of Cardio-thoracic Surgery : Official Journal of the European Association for Cardio-thoracic Surgery·Alain SerrafEmré Belli
Dec 8, 2010·Circulation·Anna N SealeUNKNOWN British Congenital Cardiac Association

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