PMID: 9189974Jan 1, 1997Paper

Anaesthetic management of children with Joubert syndrome

Paediatric Anaesthesia
W HabreM D'Souza

Abstract

We report the anaesthetic management of two children with Joubert syndrome. Children with this syndrome have abnormalities of respiratory control due to changes in the brainstem and cerebellum. They are extremely sensitive to the respiratory depressant effects of anaesthetic agents, including nitrous oxide. Anaesthesia using inhalational induction, controlled ventilation, avoidance of opioids, and close postoperative monitoring is recommended.

Citations

Jan 9, 2009·Indian Journal of Pediatrics·Suhil A ChohMajid Jehangir
Aug 5, 2000·Radiology·E J van Beek, C B Majoie
Aug 24, 2013·Journal of Clinical Anesthesia·Pradeep BhaskarAhmed Sallehuddin
Aug 2, 2006·Paediatric Anaesthesia·Cari Maria PlatisJacob Katz
Jan 8, 2013·Paediatric Anaesthesia·Sabine Buntenbroich, Alexander Dullenkopf
Jul 9, 2010·Paediatric Anaesthesia·Kamath SriganeshHanumanpura Samalingaiah Aravind
Jul 15, 2015·European Archives of Paediatric Dentistry : Official Journal of the European Academy of Paediatric Dentistry·N ChhabraS Tandon
May 22, 2010·Neurología : publicación oficial de la Sociedad Española de Neurología·P Hurtado, H Pachajoa
May 13, 2010·Journal of Child Neurology·Ari R JoffeJonathan P Duff
Sep 24, 2004·Paediatric Anaesthesia·Darko J Vodopich, Gregory J Gordon
Nov 12, 2019·American Journal of Medical Genetics. Part a·Ruxandra Bachmann-GagescuDan Doherty
Jul 1, 2009·Korean journal of anesthesiology·Yoon Sook LeeYoung Cheol Park
Jan 5, 2017·The Journal of Clinical Pediatric Dentistry·Yousr N MowafyAly A Sharaf
Apr 14, 2021·Anesthesia and Pain Medicine·Jeong Yeon KimMi Roung Jun

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