Anatomy of the ventricular septal defect in congenital heart defects: a random association?

Orphanet Journal of Rare Diseases
Meriem Mostefa-KaraDamien Bonnet

Abstract

A ventricular septal defect (VSD) is an integral part of most congenital heart defects (CHD). To determine the prevalence of VSD in various types of CHD and the distribution of their anatomic types. We reviewed 1178 heart specimens with CHD from the anatomic collection of the French Reference Centre for Complex Congenital Heart Defects. During the morphologic study a special attention was paid to the localisation of the VSD viewed from the right ventricular side. The VSDs were classified as muscular, central perimembranous, outlet located between the two limbs of the septal band, and inlet. The specimens were classified according to the 9 categories and 23 subcategories of the anatomic and clinical classification of CHD1 (ACC-CHD). Ventricular septum was almost always intact in anomalies of pulmonary veins (4/73, 5%), Ebstein anomaly (3/21, 14%), and double-inlet right ventricle (DIRV, 1/10, 10%). There was always a VSD in tetralogy of Fallot and variants (TOF, 123 cases) and common arterial trunk (CAT, 55 cases), always of the outlet type. There was almost always a VSD in double inlet left ventricle (33/34, 97%, always muscular), congenitally corrected transposition of great arteries (ccTGA, 23/24, 96%), interrupted aortic arc...Continue Reading

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Citations

Mar 15, 2019·Annals of Thoracic and Cardiovascular Surgery : Official Journal of the Association of Thoracic and Cardiovascular Surgeons of Asia·Ling-Shan YuGui-Can Zhang
Apr 5, 2019·Orphanet Journal of Rare Diseases·Justin T TretterRobert H Anderson
Sep 15, 2019·Genesis : the Journal of Genetics and Development·Yongkun ZhanGuoying Huang
Oct 20, 2020·Frontiers in Pediatrics·Ba Luu TruongYves Usson
Mar 21, 2021·Journal of Veterinary Internal Medicine·Lisa De LangeGunther van Loon
Jan 21, 2022·Birth Defects Research·Erin Bugenske StallingsUNKNOWN National Birth Defects Prevention Network

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