Anesthetic considerations in children with Hutchinson-Gilford progeria syndrome: A narrative review.

Paediatric Anaesthesia
Kristof NijsDanny Hoogma

Abstract

Hutchinson-Gilford progeria syndrome is a rare disease in childhood that results in premature aging. The presence of multisystem derangements including skin, bone, and joint diseases and possibly a difficult airway makes the anesthetic management challenging. Because of the extremely low prevalence, experience is limited even for experienced pediatric anesthesiologists. To review the available literature on anesthesia for patients with Hutchinson-Gilford progeria syndrome and to give recommendations for establishing the best practice for patients with Hutchinson-Gilford progeria syndrome. A narrative review of the rare existing literature. CENTRAL (Cochrane), EMBASE, Google Scholar, MEDLINE and PubMed. Articles addressing anesthesia in patients with Hutchinson-Gilford progeria syndrome were included. An overview of the current literature was made on anesthesia care for patients with Hutchinson-Gilford progeria syndrome. After screening the literature, only ten articles were found to be of interest and include some case reports and a correspondence. The focus points on how to perform anesthesia care in patients with Hutchinson-Gilford progeria syndrome and the entire perioperative care are suggested. The available data are limit...Continue Reading

References

Sep 1, 1979·Anesthesia and Analgesia·J W Chapin, J Kahre
Apr 6, 1999·Paediatric Anaesthesia·S KitamuraA Taniguchi
May 22, 2001·Paediatric Anaesthesia·N H Nguyen, J F Mayhew
Nov 7, 2001·Paediatric Anaesthesia·C D Liessmann
Mar 21, 2002·Paediatric Anaesthesia·T Arai, M Yamashita
Jul 22, 2009·PLoS Medicine·David MoherUNKNOWN PRISMA Group
Sep 3, 2010·Anesthesiology·Masayuki ShibasakiDaniel I Sessler
Oct 2, 2013·Journal of Pediatric Neurosciences·Upendra HansdaPragati Ganjoo
Mar 5, 2015·Paediatric Anaesthesia·R Scott HerdToby N Weingarten
Oct 22, 2016·Ageing Research Reviews·Ajoy C KarikkinethVilhelm A Bohr
Oct 18, 2016·European Journal of Anaesthesiology·Sebastiaan J M VreeswijkMark P Hendriks
Feb 22, 2018·JAMA Cardiology·Ashwin PrakashLeslie Smoot
May 2, 2018·JAMA : the Journal of the American Medical Association·Leslie B GordonMark W Kieran
Nov 12, 2018·American Journal of Human Genetics·Jennifer A WambachAbhimanyu Garg

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