Anesthetic Management in an Adult Patient With Costello Syndrome: A Case Report

A&A Practice
Kei UgataYoji Saito

Abstract

Costello syndrome is a rare genetic disorder characterized by mental and growth retardation and distinctive coarse facies. A significant proportion of patients with Costello syndrome have hypertrophic cardiomyopathy, papillomata, and malignant tumors. General anesthesia practice, especially airway and cardiac management, in patients with Costello syndrome may be complicated by anatomical features and cardiac abnormalities. There have been several reports on the anesthetic management of children with Costello syndrome, but few have reported on the anesthetic management of adults with Costello syndrome. In adults, careful preoperative evaluation as well as preparation for adult-onset and previously unrecognized medical conditions are key for safe anesthetic management.

References

Jan 1, 1997·Paediatric Anaesthesia·O Dearlove, N Harper
May 2, 2002·Paediatric Anaesthesia·F BenniG de Francisci
Mar 19, 2003·Paediatric Anaesthesia·Kelly KatcherJoseph D Tobias
Sep 24, 2004·American Journal of Medical Genetics. Part a·Patricia I DicksonHenry J Lin
Jun 9, 2005·American Journal of Medical Genetics. Part a·Susan M WhiteA Bankier
Sep 20, 2005·Nature Genetics·Yoko AokiYoichi Matsubara
Apr 13, 2012·American Journal of Medical Genetics. Part a·Yu AbeUNKNOWN Costello and CFC syndrome study group in Japan

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