Anesthetic management in Joubert syndrome

Paediatric Anaesthesia
Darko J Vodopich, Gregory J Gordon

Abstract

We review the anesthetic implications of Joubert syndrome and report that spinal anesthesia under intravenous propofol sedation proved satisfactory for repair of an inguinal hernia in a spontaneously ventilating infant with this syndrome. We caution that anatomical peculiarities may complicate performance of a caudal epidural block and suggest consideration of the use of caffeine to ameliorate the apneic episodes seen in early infancy in this syndrome.

References

Jul 1, 1992·American Journal of Medical Genetics·J M Saraiva, M Baraitser
Jan 1, 1990·Neuroradiology·B KendallP Finn
Nov 1, 1989·Anaesthesia·N C Matthews
Jan 1, 1997·Paediatric Anaesthesia·W HabreM D'Souza
May 18, 1999·Pediatric Neurology·L SztrihaM Nork
Feb 24, 2001·The Annals of Otology, Rhinology, and Laryngology·M W SungK H Kim

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Citations

Aug 24, 2013·Journal of Clinical Anesthesia·Pradeep BhaskarAhmed Sallehuddin
Aug 2, 2006·Paediatric Anaesthesia·Cari Maria PlatisJacob Katz
Jan 8, 2013·Paediatric Anaesthesia·Sabine Buntenbroich, Alexander Dullenkopf
Jul 9, 2010·Paediatric Anaesthesia·Kamath SriganeshHanumanpura Samalingaiah Aravind
Oct 18, 2016·European Journal of Anaesthesiology·Yunus O AtalayDemet Tekcan
Nov 12, 2019·American Journal of Medical Genetics. Part a·Ruxandra Bachmann-GagescuDan Doherty
Jul 1, 2009·Korean journal of anesthesiology·Yoon Sook LeeYoung Cheol Park

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