Annular atrophic lichen planus and Sneddon's syndrome

Dermatology : International Journal for Clinical and Investigative Dermatology
D LipskerC Francès

Abstract

We report the case of a patient who had 2 rare diseases, annular atrophic lichen planus (AALP) and Sneddon's syndrome (SNS). This patient had also digital nodules with histological abnormalities suggestive of SNS vasculopathy, which have not been reported so far. AALP is the most rare of all varieties of lichen planus since this case is the third reported to date. The association of livedo racemosa and cerebrovascular disease is the hallmark of SNS, the incidence of which is estimated to be 4 cases per year per million inhabitants. In both diseases, an abnormal production of elastic-tissue-degrading enzymes or a constitutional abnormality of the elastic tissue can be postulated, since SNS is characterized by arteriolar changes with deterioration of the internal elastic lamina and AALP by destruction of the dermal elastic tissue.

Citations

Mar 23, 2004·Journal of the American Academy of Dermatology·Hilary L ReichWilliam D James
Apr 7, 2016·JAAD Case Reports·Sayantani ChakrabortyRamesh C Gharami
Dec 14, 2007·Clinical and Experimental Dermatology·J-S KimH-J Yu
May 3, 2007·International Journal of Dermatology·Rosa María Ponce-OliveraPatricia Mercadillo-Pérez
Jul 31, 2007·Journal of the European Academy of Dermatology and Venereology : JEADV·B-S KimK-S Kwon
Apr 29, 2005·Journal of the American Academy of Dermatology·Ana Morales-CallaghanAlberto Miranda-Romero
Aug 29, 2019·JAMA Dermatology·Jessica G LabadieJoaquin C Brieva
Jun 12, 2020·European Journal of Neurology : the Official Journal of the European Federation of Neurological Societies·F MitriM Kraemer
Sep 26, 2021·Pediatric Dermatology·Samantha SearsPatricia Todd

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