Becker muscular dystrophy-related cardiomyopathy: a favorable response to medical therapy

The Journal of Heart and Lung Transplantation : the Official Publication of the International Society for Heart Transplantation
Anthony H DoingRuth Ann Smith

Abstract

Patients with Becker muscular dystrophy-related cardiomyopathy typically survive into their 30s, when they succumb to complications of cardiomyopathy or receive heart transplants. The cardiomyopathy is related to an abnormality in the protein dystrophin; no successful medical responses have been reported to date. We describe a patient with Becker muscular dystrophy-related cardiomyopathy in whom we noted improvement of cardiac status with carefully titrated medical therapy. Successful therapy suggests a trial of medical therapy may be beneficial when patients with Becker muscular dystrophy-related cardiomyopathy are evaluated for transplant.

References

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May 18, 1999·The Journal of Heart and Lung Transplantation : the Official Publication of the International Society for Heart Transplantation·R E ShaddyV Lemes

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Citations

Jan 19, 2013·Current Neurology and Neuroscience Reports·Louise R Rodino-KlapacZarife Sahenk
Jul 26, 2006·Circulation Journal : Official Journal of the Japanese Circulation Society·Hidemi KajimotoToshio Nakanishi
Oct 16, 2009·Journal of Medical Case Reports·Seth E WakefieldBrian S Tseng
Oct 9, 2008·The Canadian Journal of Cardiology·Josef Finsterer, Claudia Stöllberger
Jun 1, 2005·European Journal of Heart Failure·Ok Young ParkJung Chaee Kang
Jun 7, 2005·Muscle & Nerve·Fiona C Goodwin, Francesco Muntoni
May 13, 2009·Journal of the American Academy of Nurse Practitioners·Rita Wen KasparFederica Montanaro
Aug 19, 2016·International Heart Journal·Makiko NakamuraTakashi Touma
Oct 26, 2005·Circulation·John L JefferiesJeffrey A Towbin
Dec 16, 2005·Journal of Cardiovascular Magnetic Resonance : Official Journal of the Society for Cardiovascular Magnetic Resonance·Colin J PetrieHenry J Dargie

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