Bilateral carotid artery dissection due to Eagle syndrome in a patient with vascular Ehlers-Danlos syndrome: a case report

BMC Neurology
Hajime IkenouchiMasatoshi Koga

Abstract

Patients with vascular Ehlers-Danlos syndrome (EDS) occasionally suffer from arterial dissection. Eagle syndrome, which is caused by an elongated styloid process and also causes arterial dissection, is difficult to diagnose and could sometimes be overlooked. Little is known of the coexistence of these two diseases, and treatment strategy is not established. Here, we present a case of bilateral internal carotid artery (ICA) dissection due to Eagle syndrome in a patient with vascular EDS. A 30-year-old man was admitted to our hospital because of sudden onset of mild sensory disturbance in his left limbs. He had a history of Ehlers-Danlos syndrome (EDS) and also had left cervical internal carotid artery (ICA) dissection 3 years before. Diffusion-weighted imaging showed acute cerebral infarcts in the right hemisphere. Cervical computed tomography angiography (CTA) revealed the right ICA narrowing at the cervical portion in addition to the previous left cervical ICA dissection. Cervical magnetic resonance imaging (MRI) revealed double-lumen and intramural hematoma at the narrowing portion of the right cervical ICA, which indicates arterial dissection. CT also revealed bilateral elongated styloid processes which are close to each sid...Continue Reading

References

Jan 10, 2012·European Journal of Vascular and Endovascular Surgery : the Official Journal of the European Society for Vascular Surgery·M SinghD J A Scott
Oct 1, 2016·Journal of Vascular Surgery·Matthew J Eagleton
Mar 18, 2017·American Journal of Medical Genetics. Part C, Seminars in Medical Genetics·Peter H ByersNigel Wheeldon
Jun 4, 2019·World Neurosurgery·Sadaharu TorikoshiMasaki Nishimura

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Citations

Apr 26, 2021·Annals of Vascular Surgery·Enrico Nastro Siniscalchi, Giovanni Raffa
Jul 2, 2021·ENeurologicalSci·Walter R Duarte-CeladaThomas Windisch

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Methods Mentioned

BETA
dissection
surgical resection

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