Cardiac Involvement in a Patient With POEMS Syndrome Detected Using Cardiac Magnetic Resonance Imaging

International Heart Journal
Guoyuan PeiYucheng Chen

Abstract

We present a case of POEMS syndrome in which cardiac MRI (CMR) revealed cardiac involvement. POEMS syndrome is a very rare disease and cardiac involvement in POEMS syndrome is rarely reported. In the present case, echocardiography revealed left ventricular hypertrophy with moderately impaired systolic function and moderate pulmonary hypertension. CMR examination showed a typical circular subendocardial type of late gadolinium enhancement, which is a classic pattern of cardiac amyloidosis. The diagnosis of cardiac amyloidosis in POEMS would be helpful for further risk stratification and treatment strategies.

References

Apr 1, 1992·Journal of Internal Medicine·T Tanus, H J Miller
Jan 5, 2005·Circulation·Alicia Maria MaceiraDudley John Pennell
Apr 10, 2010·International Heart Journal·Katsura SomaTeruhiko Aoyagi
May 17, 2013·Internal Medicine·Tetsuro YokokawaYasuchika Takeishi
Feb 18, 2014·American Journal of Hematology·Angela Dispenzieri
Mar 19, 2014·International Heart Journal·Shin-ichi NurekiJun-ichi Kadota

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