Cardiovascular manifestations of heterotaxy and related situs abnormalities assessed with CT angiography

Journal of Cardiovascular Computed Tomography
Christopher D WollaShahryar Chowdhury

Abstract

Heterotaxy and situs abnormalities describe an abnormal arrangement of visceral organs in the thoracoabdominal cavity across the normal left-right axis of the body. It is associated with a high occurrence of congenital heart and abdominal defects, including anomalous pulmonary venous connections, systemic venous abnormalities, asplenia, and intestinal malrotation. Without proper diagnosis and surgical intervention, the prognosis of patients with heterotaxy syndrome and associated congenital defects is extremely poor. Complex intracardiac and extracardiac lesions are common in heterotaxy and can be difficult to assess by echocardiography. CT angiography (CTA) is a useful tool in this setting to accurately assess intracardiac and extracardiac abnormalities in this population for medical or surgical management. The intention of this pictorial essay is to review the most common cardiovascular defects involved with heterotaxy syndrome in addition to emphasizing the utility of CTA in the identification and classification of anomalies seen in these patients. This review briefly defines most common terminology used in situs abnormalities as well as presents CT images and 3-dimensional reconstructions of common anomalies associated with...Continue Reading

References

Apr 1, 1976·British Heart Journal·E A ShinebourneR H Anderson
Jul 1, 1985·Seminars in Roentgenology·R Van Praagh
Apr 1, 1983·Pediatric Cardiology·W M PeoplesJ E Edwards
Oct 1, 1981·AJR. American Journal of Roentgenology·J G ArciniegasL M Bargeron
Mar 1, 1982·AJR. American Journal of Roentgenology·I L Tonkin, A K Tonkin
May 23, 2007·AJR. American Journal of Roentgenology·Pierre D Maldjian, Muhamed Saric
Feb 22, 2008·Cardiology in the Young·Jeffrey P JacobsMartin J Elliott
Sep 23, 2009·AJR. American Journal of Roentgenology·Subha GhoshHugo Spindola-Franco
Mar 17, 2010·Radiographics : a Review Publication of the Radiological Society of North America, Inc·Chantale LapierreLaurent Garel
Jul 7, 2011·Korean Circulation Journal·Soo-Jin Kim
Aug 25, 2011·The American Journal of Cardiology·Joseph K Perloff
Mar 9, 2012·Journal of Cardiovascular Computed Tomography·Anu BalanEdward D Nicol

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Citations

May 11, 2015·Journal of Anesthesia·Yury RapoportAlan David Kaye
Jul 15, 2015·Cardiology in the Young·Rohit S LoombaRobert H Anderson
Jun 20, 2015·Cardiology in the Young·Rohit S LoombaRobert H Anderson
Feb 5, 2015·The Journal of Pediatrics·Filipa Flor-de-LimaHercília Guimarães
Apr 30, 2016·Journal of Ultrasound in Medicine : Official Journal of the American Institute of Ultrasound in Medicine·Richelle OlsenDolores H Pretorius
Jun 6, 2019·Pediatric Radiology·Carlos F Ugas CharcapeMonica Epelman
Aug 2, 2020·Biochimica Et Biophysica Acta. Molecular Basis of Disease·Shuzhang LiangRuilin Zhang
Mar 16, 2021·Radiology Case Reports·Habib Ahmad EsmatAsadullah Shirzai
May 15, 2021·Korean Journal of Radiology : Official Journal of the Korean Radiological Society·Hyun Woo GooDong Man Seo
Jun 8, 2021·Curēus·Pratiksha YadavNikhil B Nandivada

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