PMID: 8610226Jan 1, 1995Paper

Catastrophic anti-phospholipid syndrome in the absence of IgG anti-cardiolipin antibodies

Scandinavian Journal of Rheumatology
M KennedyE Gaffney

Abstract

The Catastrophic Anti-phospholipid Syndrome (CAPS) is a rare acute clinical syndrome associated with serum anti-phospholipid antibodies (aPL). It is rarely preceded by a precipitating event. It may occur as a primary event or be associated with auto-immune diseases. We report a fatal case occurring post-endoscopic retrograde cholangio-pancreatography (ERCP) in a patient with Systemic Lupus Erythematosus (SLE), positive lupus anticoagulant and negative IgG with positive IgM anti-cardiolipin titres. The diagnostic and therapeutic difficulties of such cases is addressed.

References

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Citations

Nov 7, 2002·Critical Care Clinics·Gloria E Westney, E Nigel Harris
Mar 11, 2009·The Journal of Rheumatology·Barbara J Rosenau, Peter H Schur

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