Chiari I malformation accompanied by assimilation of the atlas, Klippel-Feil syndrome, and syringomyelia: case report

Surgical Neurology
Masahiro KagawaSeigo Nagao

Abstract

Chiari I malformation, accompanied by superposed bony anomaly of the craniovertebral junction, is comparatively rare. We report a case of Chiari I malformation accompanied by assimilation of the atlas, Klippel-Feil syndrome, and syringomyelia. The patient was a 61-year-old woman demonstrating numbness of the extremities, sensory impairment, muscular weakness, and tendon hyper-reflexia. X-ray images and CT scans demonstrated assimilation of the atlas to the occipital bone, C2 and C3 fusion, abnormal passage of the vertebral arteries, and an anomalous bony mass on the right lateral mass of the atlas protruding into the spinal column. The odontoid process was also deviated to the left. Magnetic resonance images demonstrated bilateral descent of the cerebellar tonsils and syringomyelia extending from C6 to T8. Computed tomographic scans with the head rotated to the right demonstrated increased narrowing of the vertebral column caused by the right lateral mass of the atlas, and MR images confirmed exaggerated deformation of the spinal cord at the same region. This deformation manifested no neurologic symptoms, and we therefore performed foramen magnum decompression and duraplasty using Gore-Tex (W.L. Gore & Associates, Inc., Flagsta...Continue Reading

References

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Citations

Oct 2, 2013·Journal of Clinical Neuroscience : Official Journal of the Neurosurgical Society of Australasia·Erwin Zeta MangubatRichard W Byrne
Jun 26, 2012·Journal of Neurosurgery. Pediatrics·Robert J BolloDouglas L Brockmeyer
Sep 6, 2007·Pediatric Neurosurgery·Fuyou GuoLaijun Song
Jul 2, 2008·Journal of Neurosurgery. Spine·Albert J FenoyKathleen A Fenoy
Apr 26, 2011·Neurological Research·Ruth-Mary deSouzaDavid M Frim
Mar 29, 2008·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·Arnold H Menezes, Timothy W Vogel
Jul 16, 2019·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·Sandip ChatterjeeShyam Gopal Verma
May 14, 2021·BMJ Case Reports·Husain Abdulameer AbdaliAlmughirah Salahaldin Mohamed

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