Chronic thromboembolic pulmonary hypertension: an enigma

BMJ Case Reports
Suraj Kumar KulkarniPrakash Sadashivappa Surhonne

Abstract

Chronic thromboembolic pulmonary hypertension (CTEPH) is a form of pulmonary arterial hypertension (PAH) in which the pulmonary thrombus fails to resolve, resulting in occlusion and remodelling of pulmonary arteries.1 Timely diagnosis is critical since it is potentially curable by pulmonary thromboendarterectomy. Twenty five per cent of cases do not have a history of thromboembolic event. The diagnosis should be considered in the diagnostic work-up of PAH despite lack of history of episodes of thromboembolism. Here we are reporting a case of CTEPH with multiple systemic to pulmonary collaterals delineated by angiogram and CT.

References

May 28, 2004·The New England Journal of Medicine·Vittorio PengoUNKNOWN Thromboembolic Pulmonary Hypertension Study Group
Aug 19, 2007·Heart·Keith McNeil, John Dunning
Feb 6, 2009·Thrombosis Research·Francesco DentaliWalter Ageno
Mar 2, 2012·European Respiratory Review : an Official Journal of the European Respiratory Society·N H Kim, I M Lang
Jun 2, 2015·European Respiratory Review : an Official Journal of the European Respiratory Society·Andrea M D'Armini

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