Clinical implications and possible association of malposition of the branch pulmonary arteries with DiGeorge syndrome and microdeletion of chromosomal region 22q11

The American Journal of Cardiology
M R RectoW W Lai

Abstract

We describe a series of 10 patients with malposition of the branch pulmonary arteries (4 patients with crossing [crossed pulmonary arteries] and 6 patients without crossing), 2 of whom had a short main pulmonary artery segment that resulted in iatrogenic right pulmonary artery stenosis after pulmonary artery band placement. DiGeorge syndrome was seen in 5 patients and 4 had microscopic deletion of chromosomal region 22q11.

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Citations

Apr 11, 2008·Journal of the Formosan Medical Association = Taiwan Yi Zhi·Bang-Bin ChenMei-Hwan Wu
Jun 23, 2001·Journal of the American College of Cardiology·D B McElhinneyE Goldmuntz
Jun 24, 2014·Cardiology in the Young·Lazaro E HernandezCharles W Shepard
Apr 30, 2014·Cardiology in the Young·Jennifer E TingoMatthew A Crystal
Jul 19, 2008·Developmental Disabilities Research Reviews·Adriano CarottiBruno Marino
Aug 29, 2012·Pediatric Cardiology·Ryo AebaRyohei Yozu
Mar 11, 2021·Pediatric Radiology·André VazBruno Maurício Pedrazzani
May 25, 2010·The American Journal of Cardiology·Kazuo Momma
May 3, 2003·International Journal of Cardiology·Jesse Li-Ling

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