Cochlear Implantation in a Patient With Pfeiffer Syndrome and Temporal Bone Vascular Anomalies

Otology & Neurotology : Official Publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
Samuel R BarberAlicia M Quesnel

Abstract

Pfeiffer syndrome is a rare craniosynostotic disorder resulting in premature bony fusion of the skull, which can result in abnormal temporal bone and vascular anatomy and hearing loss. Cochlear implantation in these patients requires thoughtful surgical planning given the potential for limited access to the cochlea because of subcutaneous or intratemporal vasculature. Herein, we present a patient with Pfeiffer syndrome who underwent successful cochlear implantation using preoperative Doppler ultrasound to identify large extracranial venous anatomy followed by a modified transcanal surgical approach. An adult female patient with Pfeiffer syndrome. Preoperative axial computed tomography, catheter angiography, Doppler ultrasound, and right side cochlear implant. Surgical feasibility and audiometric outcomes including aided thresholds and word recognition score. Successful cochlear implantation was performed via a modified transcanal approach with blind sac closure of the external auditory meatus. Full electrode insertion was obtained through a round window approach. No extracranial or intratemporal vessels were encountered during surgery. Patients with significant craniosynostoses and vascular malformations of the temporal bone ca...Continue Reading

References

May 29, 2000·The Journal of Laryngology and Otology. Supplement·J M GrahamL Michaels
Jan 5, 2002·The Cleft Palate-craniofacial Journal : Official Publication of the American Cleft Palate-Craniofacial Association·Samson LeeMichael Cunningham
May 7, 2004·Otology & Neurotology : Official Publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology·Emmanuel A M MylanusRens L Leeuw
Jun 3, 2006·Orphanet Journal of Rare Diseases·Annick Vogels, Jean-Pierre Fryns
Sep 22, 2010·The Journal of Craniofacial Surgery·Urmen DesaiGary F Rogers
Feb 9, 2012·The Laryngoscope·David R FriedmannAnil K Lalwani
Aug 21, 2014·Otology & Neurotology : Official Publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology·Abdulrahman DiaMiriam Redleaf

❮ Previous
Next ❯

Citations

Jul 12, 2019·Otology & Neurotology : Official Publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology·Noor-E-Seher AliNikolas H Blevins
Oct 22, 2020·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·Ioannis N Mavridis, Desiderio Rodrigues
Jan 30, 2021·The Annals of Otology, Rhinology, and Laryngology·Tiffany P HwaAnil K Lalwani
Jun 30, 2021·The Journal of Maternal-fetal & Neonatal Medicine : the Official Journal of the European Association of Perinatal Medicine, the Federation of Asia and Oceania Perinatal Societies, the International Society of Perinatal Obstetricians·Antonella VimercatiEttore Cicinelli

❮ Previous
Next ❯

Methods Mentioned

BETA
cochlear implant
dissect
dissection

Software Mentioned

Flex

Related Concepts

Related Feeds

Auditory Perception

Auditory perception is the ability to receive and interpret information attained by the ears. Here is the latest research on factors and underlying mechanisms that influence auditory perception.

Related Papers

Journal of Surgical Case Reports
E IacovouJ Xenelis
Otology & Neurotology : Official Publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
Abdulrahman DiaMiriam Redleaf
The American Journal of Otology
T P NikolopoulosK P Gibbin
Otology & Neurotology : Official Publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
Yiqing ZhengMichael M Paparella
© 2021 Meta ULC. All rights reserved