Complement deficiency states

The Alternative Complement Pathway is part of the innate immune system, and activation generates membrane attack complexes that kill pathogenic cells. Discover the latest research on the Alternative Complement Pathway.

Complement deficiency states

Abstract

Citations

Participation of factor B in residual immune complex red cell binding activity observed in serum from a C2-deficient systemic lupus erythematosus patient may delay the appearance of clinical symptoms

Association of systemic lupus erythematosus and SLE-like syndromes with hereditary and acquired complement deficiency states

Factor XII deficiency with systemic lupus erythematosus. Biological implications

Early complement component depletion and mixed cryoglobulinemia in a "healthy" family

Polyarthritis in a 78-year-old woman

Further study on a BF silent allele

Renal disease and vasculitis

Lupus nephritis in childhood and adolescence

Recurrent pyogenic infections in individuals with absence of the second component of complement

Inherited deficiency of C8 in a patient with recurrent meningococcal infections: further evidence for a dysfunctional C8 molecule and nonlinkage to the HLA system

Hereditary angioedema and aortitis

Inherited deficiencies of complement proteins in man

Lupus diseases associated with hereditary and acquired deficiencies of complement

Systemic lupus erythematosus

Genetic deficiency of C4 presenting with recurrent infections and a SLE-like disease. Genetic and immunologic studies

Binding of complement components C1q, C3, C4 and C5 to a model immune complex in ELISA.

Immunology of renal transplantation

HLA and disease

Laboratory techniques of veterinary clinical immunology: a review

Membrane attack by complement

Total hemolytic complement values in normal and diseased dog populations

Complement levels in dogs with familial canine dermatomyositis

Lupus erythematosus

An enzyme based assay for the measurement of complement mediated binding of immune complexes to red blood cells

Increased susceptibility to severe pyogenic infections in patients with an inherited deficiency of the second component of complement

Complement, the immune-complex lattice, and the pathophysiology of complement-deficiency syndromes

Coming to terms with complement

Genetically determined low C4: a predisposing factor to autoimmune chronic active hepatitis

Gene and haplotype frequencies of the fourth component of complement (C4) in type 1 diabetics and normal controls

Systemic lupus erythematosus in hereditary deficiency of the fourth component of complement

Significance of the anti-Ro (SS-A) antibody in evaluation of patients with cutaneous manifestations of a connective tissue disease

The molecular genetics of components of the complement system

Hypocomplementemic urticarial vasculitis syndrome. Clinical and serologic findings in 18 patients

Clinical features and metabolic and autoimmune derangements in acquired partial lipodystrophy: report of 35 cases and review of the literature

Systemic lupus erythematosus complicating complement type 2 deficiency: successful treatment with fresh frozen plasma

The normocomplementemic urticarial vasculitis syndrome--report of a case and response to colchicine

Changes in immunologic response in tonsillectomized children. I. Immunosuppression in recurrent tonsillitis

Increased amounts of C4-containing immune complexes and inefficient activation of C3 and the terminal complement pathway in a patient with homozygous C2 deficiency and systemic lupus erythematosus

Systemic meningococcal infections in patients with acquired complement deficiency

Polymorphism of the second component of human complement (C2). Observation of the rare phenotype (C2 2 (= C2 B) and data on the localization of the C2 locus in the HLA region

Effect of age on serum concentrations of the third component of complement in dogs

Combined hepatocellular-cholangiocarcinoma associated with dermatomyositis

Childhood subacute cutaneous lupus erythematosus associated with homozygous complement 2 deficiency

A polymorph bactericidal defect and a lupus-like syndrome

Deficiency of the second complement component association with the HLA haplotype A10, B18 in a normal population

Terminal complement component deficiencies and rheumatic disease: development of a rheumatic syndrome and anticomplementary activity in a patient with complete C6 deficiency

Heterozygous C2 deficiency associated with angioedema, myasthenia gravis, and systemic lupus erythematosus

SLE-like and sicca symptoms in late component (C9) complement deficiency

Complement factor 2 deficiency: a clinical and serological family study

Serum complement component depression during acute adenovirus conjunctivitis

Related Concepts

Related Feeds

Alternative Complement Pathway

Related Papers

Inherited deficiency of the second component of complement. Rheumatic disease associations

Lupus-erythematosus-like disease in three unrelated women with hereditary angioneurotic edema.

Inherited structural polymorphism of the fourth component of human complement

Hereditary angioedema and "familial" lupus erythematosus in identical twin boys

The complement system in chronic glomerulonephritis: three newly associated aberrations