PMID: 7095905Jan 1, 1982

Congenital absence of the pulmonary valve leaflets associated with complete transposition of the great arteries

International Journal of Cardiology
J OvseyevitzA Buendia


We describe the clinical and surgical findings of a patient with absence of the pulmonary valve leaflets and complete transposition of the great arteries. The main clinical features were a loud, single second heart sound, a loud pansystolic murmur over the entire precordial area, but no diastolic murmurs were heard. The electrocardiogram suggested right ventricular hypertrophy and right bundle branch block. The roentgenographic study showed cardiomegaly with dilatation of both branches of the pulmonary artery. Cardiac catheterization and angiocardiography showed systemic arterial desaturation, discordant ventriculo-arterial connections and absence of the pulmonary valve leaflets. The patient underwent surgical correction by the Rastelli technique with a favorable clinical course.


Jan 1, 1978·Circulation·W W PinskyD G McNamara
Mar 4, 1976·The American Journal of Cardiology·G C EmmanoulidesM Fishbein
May 1, 1969·The American Journal of Roentgenology, Radium Therapy, and Nuclear Medicine·M Z OsmanB R Girdany
Apr 1, 1964·Circulation·R W CHILDERS, P C MCCREA


Jun 1, 2001·The Annals of Thoracic Surgery·G OppidoR M Di Donato
Mar 1, 1997·Echocardiography·Orathai PachiratPatrick W. O'leary
Jul 1, 1983·British Heart Journal·A BuendiaR Richheimer
Mar 1, 1994·The British Journal of Radiology·C M OwensD Shaw
Feb 1, 1984·International Journal of Cardiology·A M Tenorio de AlbuquerqueF Pileggi
Jan 1, 1987·Heart and Vessels·K NiwaM Ando
May 24, 2019·World Journal for Pediatric & Congenital Heart Surgery·Ashish KatewaShivani Gajpal

Related Concepts

Diastolic Blood Pressure
2D Echocardiography
Electrocardiographic Recorders
Cardiac Catheterization Procedures
Ventricular Septal Defects
Left Ventricular Structure
Pulmonary Artery Structure
Pulmonary Valve Structure
Transposition of Great Vessels

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