PMID: 9436846Jan 22, 1998Paper

Dermatofibrosarcoma protuberans in childhood

Pediatric Dermatology
M L Bouyssou-GauthierJ M Bonnetblanc

Abstract

Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous tumor with a possibly misleading presentation. It is rare in childhood. We report an 18-month-old child with an acquired atrophic plaque of the left ankle. Based on clinical findings, initial proposed diagnoses included localized scleroderma and localized lipoatrophy. At the age of 5 years the plaque had increased in size and become a purplish color. Several firm nodules were seen at its periphery. A diagnosis of DFSP was proposed and confirmed histologically. A large surgical resection was performed. This case illustrates that DFSP may occur in childhood, during which initial diagnosis is generally more difficult than in adulthood.

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Citations

Oct 31, 2000·Radiotherapy and Oncology : Journal of the European Society for Therapeutic Radiology and Oncology·L M SunS P Lee
Oct 27, 2001·International Journal of Dermatology·M MariniL Remorino
Oct 26, 2007·Pediatric Dermatology·Jennie T ClarkeAndrea L Zaenglein
Jun 26, 2008·Pediatric Dermatology·Fatemeh JafarianBourouia Ben Nejma
Jan 29, 2005·American Journal of Clinical Dermatology·Iqbal BukhariYousef Bedaiwi
Nov 17, 2012·Actas dermo-sifiliográficas·M Valdivielso-Ramos, J M Hernanz
Apr 10, 2012·Actas dermo-sifiliográficas·M Valdivielso-Ramos, J M Hernanz
Jul 16, 2013·Pediatric Dermatology·Ann L MarquelingIlona J Frieden
Apr 18, 2000·Journal of the American Academy of Dermatology·S R CheckettsR D Baughman
Jun 21, 2005·Journal of the American Academy of Dermatology·Sharon Longshore ThorntonAllison T Vidimos
Jun 6, 2002·Journal of the European Academy of Dermatology and Venereology : JEADV·M NavarroA Aliaga
Jul 15, 2004·The Australasian Journal of Dermatology·Jason K WuConleth Anthony Egan
Aug 11, 2006·Journal of the European Academy of Dermatology and Venereology : JEADV·A FidalgoR Bajanca
Jun 15, 2005·Dermatologic Therapy·Davis FarvoldenKaren Wiss
Mar 27, 2013·Journal of Pediatric Hematology/oncology·Ausilia M ManganoniPiergiacomo Calzavara-Pinton
Nov 14, 2002·Journal of the European Academy of Dermatology and Venereology : JEADV·R Oliveira-SoaresA Picoto

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