PMID: 9021579Jan 1, 1997Paper

Digestive tract disorders associated with asplenia/polysplenia syndrome

Journal of Pediatric Surgery
K NakadaN Yamate

Abstract

The authors reviewed experience gained over a 20-year period of asplenia or polysplenia syndrome, focusing on patients with associated digestive tract disorders (DTDs). Eleven of 27 patients (40%) with asplenia/polysplenia had associated DTDs. The DTDs comprised malrotation of the intestine in nine, both preduodenal portal vein and gastric volvulus in three, esophageal hiatal hernia in two, and biliary atresia in one. Laparotomy was carried out on four patients with symptoms of acute bowel obstruction and on one patient with biliary atresia. One patient with both malrotation and gastric volvulus, and another with only associated malrotation survived. Nine patients died, eight of cardiac insufficiency and one because of hepatic insufficiency. When infants are diagnosed with heterotaxia, they should be examined for other combined DTDs, because they may have a chance for survival if they undergo surgery when their condition is still stable.

Citations

May 31, 2012·Pediatric Cardiology·Charissa R PockettLindsay M Ryerson
Apr 29, 2004·Pediatric Surgery International·Abid Qazi, Sami Awadalla
Sep 18, 2007·Pediatric Surgery International·Ahmed H Al-Salem
Aug 29, 2006·Surgery Today·Kazuhide MatsushimaMasanori Gushimiyagi
May 3, 2003·International Journal of Cardiology·Jesse Li-Ling
Feb 26, 2000·Molecular Medicine Today·I Capdevila, J C Izpisúa Belmonte
Oct 6, 2005·Acta Paediatrica·Jui-Yu HsuMei-Hwan Wu
May 25, 2006·Current Opinion in Pediatrics·S H Borenstein, J C Langer
May 14, 2005·Archives of Disease in Childhood·M ChoiJ C Langer
Oct 27, 2004·Medicinski pregled·Milan Jovanović, Jovica Jovanović
Aug 3, 2012·Journal of the American Veterinary Medical Association·Andrew M GrangeSue A Casale
Nov 15, 2008·World Journal of Gastroenterology : WJG·Hyung-Il SeoSuk Kim
Feb 13, 2016·Cardiovascular Pathology : the Official Journal of the Society for Cardiovascular Pathology·Rohit S LoombaRobert H Anderson
Mar 6, 2007·Journal of Pediatric Surgery·David B TashjianRobert J Touloukian
Sep 29, 2015·Journal of Pediatric Surgery·Paul S CullisPaul D Losty
Mar 19, 2015·Journal of Pediatric Surgery·Arash SalavitabarWyman W Lai
Aug 18, 2004·Pediatrics International : Official Journal of the Japan Pediatric Society·Chin-Ying YangYen-Hsuan Ni
Jun 26, 2003·Journal of Medical Primatology·M M JenebyD Chai
Aug 25, 2011·The American Journal of Cardiology·Joseph K Perloff
May 20, 2015·American Journal of Transplantation : Official Journal of the American Society of Transplantation and the American Society of Transplant Surgeons·C J E Watson, S J F Harper
Sep 19, 2000·The Journal of Veterinary Medical Science·H KayanumaS Sato
Oct 8, 2013·Journal of Pediatric Surgery·Charissa R PockettLindsay M Ryerson
Jun 4, 2014·Journal of Pediatric Surgery·Sarah J HillMark L Wulkan
Apr 15, 2015·World Journal for Pediatric & Congenital Heart Surgery·Zeena MakhijaRajesh Sharma
Sep 10, 2016·World Journal of Clinical Pediatrics·Kurt D PiggottWilliam Decampli
Sep 27, 2005·Ultrasound in Obstetrics & Gynecology : the Official Journal of the International Society of Ultrasound in Obstetrics and Gynecology·C BergU Gembruch
Nov 18, 2003·Ultrasound in Obstetrics & Gynecology : the Official Journal of the International Society of Ultrasound in Obstetrics and Gynecology·C BergA A Baschat
Jun 3, 2014·Obstetrics & Gynecology Science·Mi-Young LeeAhm Kim
Jun 21, 2006·Developmental Dynamics : an Official Publication of the American Association of Anatomists·Kristen LipscombNanette Nascone-Yoder
Mar 22, 2002·Pediatric Transplantation·Toshimichi HasegawaAkira Okada
May 1, 2019·Ultrasound : Journal of the British Medical Ultrasound Society·Madhavilatha Routhu, Imran Ali Mohammad
Apr 19, 2015·Current Opinion in Pediatrics·Daniel L LodwickKatherine J Deans
Jun 13, 2017·Ultrasound in Obstetrics & Gynecology : the Official Journal of the International Society of Ultrasound in Obstetrics and Gynecology·D I P BucaF D'Antonio
Apr 3, 2021·Journal of Cardiovascular Development and Disease·Catherine C PickinAdrian Crucean
May 31, 2021·The American Journal of the Medical Sciences·Muhammad SoofiVaskar Mukerji

Related Concepts

Related Feeds

Birth Defects

Birth defects encompass structural and functional alterations that occur during embryonic or fetal development and are present since birth. The cause may be genetic, environmental or unknown and can result in physical and/or mental impairment. Here is the latest research on birth defects.