PMID: 11606861Oct 19, 2001Paper

Duodenal somatostatinoma presenting with complete somatostatinoma syndrome

Journal of Clinical Gastroenterology
B T Green, D C Rockey

Abstract

Somatostatinomas are the rarest pancreatic endocrine tumors and can arise in the pancreas or duodenum. Duodenal somatostatinomas are less common than, and are distinguished from, their pancreatic counterparts by a frequent association with type I neurofibromatosis, the presence of psammoma bodies, the less frequent presence of metastatic disease, and the absence of somatostatinoma syndrome (diabetes mellitus, steatorrhea, and cholelithiasis). We report a case of somatostatinoma with metastases and psammoma bodies presenting with all three features of the syndrome in a patient with neurofibromatosis. Although several reports have documented portions of the syndrome in patients with duodenal somatostatinomas, to our knowledge, this is the first report of the complete syndrome associated with a duodenal lesion.

References

Aug 9, 1979·The New England Journal of Medicine·G J KrejsR H Unger
Jun 1, 1990·Current Problems in Surgery·E MozellT M O'Dorisio
May 1, 1986·The American Journal of Surgical Pathology·Y DayalH J Wolfe
Sep 1, 1987·Journal of Surgical Oncology·G J HarrisA B Cruz
Oct 1, 1983·The American Journal of Surgical Pathology·Y DayalH J Wolfe
Feb 1, 1984·The British Journal of Surgery·S L JensenJ J Holst
May 1, 1994·Journal of Computer Assisted Tomography·R T Tjon A ThamC B Lamers
Jan 25, 1996·The New England Journal of Medicine·S W LambertsL J Hofland
Dec 31, 1998·European Journal of Surgical Oncology : the Journal of the European Society of Surgical Oncology and the British Association of Surgical Oncology·F FulfaroC Ripamonti

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Citations

Sep 13, 2006·Digestive Diseases and Sciences·G GuercioniE Landi
Mar 20, 2010·Journal of Gastrointestinal Surgery : Official Journal of the Society for Surgery of the Alimentary Tract·Daniel RellesCharles J Yeo
Dec 4, 2003·Journal of Clinical Pathology·S A PaiU V Rao
Feb 22, 2007·Neuroendocrinology·Robert T JensenUNKNOWN European Neuroendocrine Tumor Society
Jan 21, 2012·Neuroendocrinology·Gianfranco Delle FaveUNKNOWN Barcelona Consensus Conference participants
Jan 14, 2012·The Oncologist·Sachin Patil, Ronald S Chamberlain
Dec 10, 2009·World Journal of Gastroenterology : WJG·Radoje B ColovićStojan M Latincić
Oct 1, 2009·Journal of Cytology·Us DineshRavikala Rao
Jul 25, 2007·Journal of Gastroenterology and Hepatology·Gabriella NesiFrancesco Tonelli
Jun 3, 2004·The Journal of Surgical Research·John C Mansour, Herbert Chen
Apr 26, 2005·Pancreatology : Official Journal of the International Association of Pancreatology (IAP) ... [et Al.]·George MarakisAthanassios Sakadamis
Apr 16, 2013·Best Practice & Research. Clinical Gastroenterology·Dermot O'TooleRobert T Jensen
Jan 28, 2017·Clinical Gastroenterology and Hepatology : the Official Clinical Practice Journal of the American Gastroenterological Association·Majid AlsahafiFergal Donnellan
May 14, 2005·Journal of Computer Assisted Tomography·Jennifer M HendiElliot K Fishman
May 26, 2010·Endocrine Practice : Official Journal of the American College of Endocrinology and the American Association of Clinical Endocrinologists·Aikaterini TheodorakiPierre-Marc Gilles Bouloux
Aug 12, 2006·Endocrine Practice : Official Journal of the American College of Endocrinology and the American Association of Clinical Endocrinologists·Baback MoayedoddinVahab Fatourechi

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