PMID: 8736407Apr 1, 1996Paper

Encephaloduroarterio-synangiosis in a child with sickle cell anemia and moyamoya disease

Pediatric Neurology
O VernetJ P Farmer

Abstract

We report a black girl with sickle cell anemia. On prophylactic exchange transfusion protocol, she experienced cerebrovascular accidents at 3 and 3.5 years of age, both associated with transient right hemiparesis. At 7.5 years of age, she presented with a partial motor seizure and a left hemiparesis. A cerebral angiogram demonstrated stenosis at the origins of both middle and anterior cerebral arteries bilaterally with extensive basal collateralization. She underwent uncomplicated bilateral encephaloduroarteriosynangiosis (EDAS) procedures using both superficial temporal arteries. At age 9 years, the patient presented with a severe headache and tunnel vision secondary to a stenosis of both posterior cerebral arteries. She underwent bilateral EDAS procedures using both occipital arteries. No complication was encountered. Postoperative cerebral angiogram demonstrated impressive neovascularity at the sites of all four EDAS procedures. Different treatment options of moyamoya disease are discussed.

References

Mar 1, 1979·Journal of Neurology, Neurosurgery, and Psychiatry·T KitaharaY Maki
Jan 1, 1979·Child's Brain·K RajakulasingamA J Raimondi
Nov 1, 1978·Journal of Neurosurgery·J KarasawaT Sakaki
Nov 1, 1978·The Journal of Pediatrics·R A SeelerH R Goldberg
Sep 21, 1976·Neuroradiology·T A TomsickC Benton
Dec 1, 1989·Stroke; a Journal of Cerebral Circulation·G M de Courten-MyersR E Myers
Jan 1, 1986·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·K FujitaS Matsumoto
Jun 1, 1969·The American Journal of Roentgenology, Radium Therapy, and Nuclear Medicine·J M Taveras
Oct 26, 1972·The New England Journal of Medicine·J A StockmanF A Oski
Oct 1, 1970·Neurology·N T MathewJ Chandy
Nov 1, 1965·Journal of Neurosurgery·M L Cheatham, C E Brackett
Jan 1, 1983·Stroke; a Journal of Cerebral Circulation·J Suzuki, N Kodama
Jan 1, 1995·Pediatric Neurosurgery·P D Adelson, R M Scott
Oct 8, 2011·Stroke; a Journal of Cerebral Circulation·Paritosh Pandey, Gary K Steinberg

❮ Previous
Next ❯

Citations

Jul 12, 2002·Annals of Neurology·Mara PrenglerRobert J Adams
Jul 29, 2004·Current Treatment Options in Neurology·Fenella J. Kirkham, Michael R. DeBaun
Oct 29, 2003·Pediatric Neurology·Robert H FryerNeil A Feldstein
May 3, 2000·British Journal of Haematology·D R Powars
Mar 21, 2008·Journal of Neurosurgery. Pediatrics·Todd C HankinsonRichard C E Anderson
Apr 27, 2016·Journal of Neurosciences in Rural Practice·Satyakam Mohapatra, Alok Jyoti Sahoo
Jan 1, 2011·Case Reports in Neurological Medicine·Jagdish P GoyalSangita Trivedi
Jun 16, 2017·British Journal of Neurosurgery·Alexander AlamriChristos M Tolias
Mar 30, 2010·Acta neurochirurgica·Imran LiaquatPeter R Bullock
Nov 28, 2001·Hematology·R J AdamsW Wang
Mar 4, 2000·Current Opinion in Hematology·R J Adams
Jun 21, 2013·Expert Review of Hematology·Jennifer Webb, Janet L Kwiatkowski
Nov 25, 2003·Hematology·George F AtwehRobert J Adams

❮ Previous
Next ❯

Related Concepts

Related Feeds

Blood And Marrow Transplantation

The use of hematopoietic stem cell transplantation or blood and marrow transplantation (bmt) is on the increase worldwide. BMT is used to replace damaged or destroyed bone marrow with healthy bone marrow stem cells. Here is the latest research on bone and marrow transplantation.

Anemia

Anemia develops when your blood lacks enough healthy red blood cells. Anemia of inflammation (AI, also called anemia of chronic disease) is a common, typically normocytic, normochromic anemia that is caused by an underlying inflammatory disease. Here is the latest research on anemia.

Aphasia

Aphasia affects the ability to process language, including formulation and comprehension of language and speech, as well as the ability to read or write. Here is the latest research on aphasia.