Epilepsy in the nevoid basal-cell carcinoma syndrome (Gorlin syndrome): report of a case due to a focal neuronal heterotopia

Neurology
R E HoganM J Cook

Abstract

We present a case of uncontrolled temporal lobe epilepsy due to a focal left temporal neuronal heterotopia associated with the nevoid-basal-cell carcinoma syndrome. This is the first pathologically described lesion associated with temporal lobe epilepsy in this syndrome. Because the patient's seizures resolved after a modified left anterior temporal lobectomy, this case illustrates that epilepsy in patients with the nevoid basal-cell carcinoma syndrome is potentially curable and should be investigated appropriately.

Citations

Nov 17, 2004·Genetics in Medicine : Official Journal of the American College of Medical Genetics·Robert J Gorlin
Nov 27, 2008·Orphanet Journal of Rare Diseases·Lorenzo Lo Muzio
Oct 12, 2007·Journal of Oral Science·Ataollah HabibiMorteza Habibi
Sep 27, 2008·Journal of Oral Science·Binali CakurNesrin Gürsan
Oct 24, 2007·Pediatric Neurology·Nobutada TachiToshiyuki Miyashita
Jul 10, 2004·International Journal of Paediatric Dentistry·G BakaeenN D Dallal

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