Fetal Type Rhabdomyoma of the Soft Palate in an Adult Patient: Report of One Case and Review of the Literature

Head and Neck Pathology
Zhenjian CaiHui Zhu

Abstract

Rhabdomyoma is a rare benign tumor with skeletal muscle differentiation. Rhabdomyoma is further classified into cardiac, adult, fetal, and genital subtypes. Out of these, fetal type rhabdomyoma (FTR) is the rarest. Only a small number of cases have been recorded in the literature. FTR typically affects male infants and young children and occurs predominantly in the head and neck region. FTR is exceedingly rare in the adult, with less than 30 cases reported. The classic FTR is composed of primitive undifferentiated spindle cells with scant eosinophilic cytoplasm embedded in a myxoid stroma. Immunohistochemically, the tumor cells are positive for desmin, muscle specific actin, and myogenin. Awareness and proper recognition of this rare entity is of considerable importance to avoid misdiagnosis of embryonal rhabdomyosarcoma. In this study, we report one case of FTR in an adult patient and reviewed the literature about the clinical and pathologic presentation of FTR in the adult.

References

Nov 1, 1975·The Journal of Laryngology and Otology·A Ferlito, P Frugoni
Jul 1, 1972·Cancer·L P DehnerR L Font
Jul 1, 1983·Human Pathology·P M BaleM M Stevens
Feb 1, 1993·Gynecologic Oncology·S M JacquesV K Malviya
Jan 1, 1958·The Journal of Pathology and Bacteriology·K A MISCH
Aug 13, 2005·Fetal and Pediatric Pathology·M VinaitheerthanE Gilbert Barness
Sep 1, 2005·Virchows Archiv : an International Journal of Pathology·Torsten Hansen, Detlef Katenkamp
Feb 28, 2008·The American Journal of Surgical Pathology·Sarah N Walsh, Mark A Hurt
Nov 6, 2012·European Archives of Oto-rhino-laryngology : Official Journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : Affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery·Shachi J SharmaClaus Wittekindt
Jan 5, 2014·Modern Pathology : an Official Journal of the United States and Canadian Academy of Pathology, Inc·Andrew L Folpe
Jul 13, 2017·International Journal of Gynecological Pathology : Official Journal of the International Society of Gynecological Pathologists·J Kenneth SchoolmeesterWilliam R Sukov
Dec 11, 2017·Urologia Internationalis·L González-PérezE Salido Ruiz

❮ Previous
Next ❯

Citations

Mar 9, 2021·Pediatric and Developmental Pathology : the Official Journal of the Society for Pediatric Pathology and the Paediatric Pathology Society·Lara BerkliteRita Alaggio
Jan 19, 2022·Der Hautarzt; Zeitschrift für Dermatologie, Venerologie, und verwandte Gebiete·Alexandra-Irina ButacuGeorge-Sorin Tiplica

❮ Previous
Next ❯

Related Concepts

Trending Feeds

COVID-19

Coronaviruses encompass a large family of viruses that cause the common cold as well as more serious diseases, such as the ongoing outbreak of coronavirus disease 2019 (COVID-19; formally known as 2019-nCoV). Coronaviruses can spread from animals to humans; symptoms include fever, cough, shortness of breath, and breathing difficulties; in more severe cases, infection can lead to death. This feed covers recent research on COVID-19.

Blastomycosis

Blastomycosis fungal infections spread through inhaling Blastomyces dermatitidis spores. Discover the latest research on blastomycosis fungal infections here.

Nuclear Pore Complex in ALS/FTD

Alterations in nucleocytoplasmic transport, controlled by the nuclear pore complex, may be involved in the pathomechanism underlying multiple neurodegenerative diseases including Amyotrophic Lateral Sclerosis and Frontotemporal Dementia. Here is the latest research on the nuclear pore complex in ALS and FTD.

Applications of Molecular Barcoding

The concept of molecular barcoding is that each original DNA or RNA molecule is attached to a unique sequence barcode. Sequence reads having different barcodes represent different original molecules, while sequence reads having the same barcode are results of PCR duplication from one original molecule. Discover the latest research on molecular barcoding here.

Chronic Fatigue Syndrome

Chronic fatigue syndrome is a disease characterized by unexplained disabling fatigue; the pathology of which is incompletely understood. Discover the latest research on chronic fatigue syndrome here.

Evolution of Pluripotency

Pluripotency refers to the ability of a cell to develop into three primary germ cell layers of the embryo. This feed focuses on the mechanisms that underlie the evolution of pluripotency. Here is the latest research.

Position Effect Variegation

Position Effect Variagation occurs when a gene is inactivated due to its positioning near heterochromatic regions within a chromosome. Discover the latest research on Position Effect Variagation here.

STING Receptor Agonists

Stimulator of IFN genes (STING) are a group of transmembrane proteins that are involved in the induction of type I interferon that is important in the innate immune response. The stimulation of STING has been an active area of research in the treatment of cancer and infectious diseases. Here is the latest research on STING receptor agonists.

Microbicide

Microbicides are products that can be applied to vaginal or rectal mucosal surfaces with the goal of preventing, or at least significantly reducing, the transmission of sexually transmitted infections. Here is the latest research on microbicides.

Related Papers

Zhonghua bing li xue za zhi Chinese journal of pathology
Qiuyan SunJian Wang
Case Reports in Dentistry
Ana Amelia SouzaAndresa Borges Soares
© 2022 Meta ULC. All rights reserved