Hereditary angioedema

Der Internist
Emel Aygören-Pürsün, Konrad Bork

Abstract

Hereditary angioedema (HAE) encompasses a heterogeneous group of diseases with similar phenotypes but different underlying genotypes. Specific clinical signs may point to HAE as opposed to histaminergic angioedema: the typical prolonged development of angioedema over time, positive family history, a lack of response to antihistamines and steroids and response to bradykinin antagonists are typical signs of HAE. The different types of HAE may be associated with a severe clinical course. They are life-long conditions and are still potentially life-threatening. The quality of life of patients with HAE may be considerably impaired. Management plans should be individualized, which is facilitated by the variety of specific medicastions available.

References

Feb 9, 2006·The American Journal of Gastroenterology·Konrad BorkJochen Hardt
Apr 28, 2006·Biochemical and Biophysical Research Communications·Georg Dewald, Konrad Bork
Jul 31, 2012·The Journal of Allergy and Clinical Immunology·Konrad BorkGünther Witzke
Feb 8, 2013·PloS One·Marcus MaurerUNKNOWN I O S Investigators
Nov 26, 2013·Allergy and Asthma Proceedings·Teresa CaballeroHenrik B Boysen
Jul 6, 2014·Orphanet Journal of Rare Diseases·Emel Aygören-PürsünTeresa Caballero
Apr 27, 2016·Clinical Reviews in Allergy & Immunology·Anastasios E Germenis, Matthaios Speletas
May 1, 2016·The Journal of Allergy and Clinical Immunology·Steven de MaatCoen Maas
Jun 16, 2016·The Journal of Allergy and Clinical Immunology·Emel Aygören-PürsünMarcus Maurer
Sep 24, 2016·Patient Preference and Adherence·Emel Aygören-PürsünTeresa Caballero
Mar 23, 2017·The New England Journal of Medicine·Hilary LonghurstUNKNOWN COMPACT Investigators
Jun 12, 2017·The Journal of Allergy and Clinical Immunology·Valeria BafunnoMaurizio Margaglione
Aug 22, 2017·Frontiers in Medicine·Fabrício Simão, Edward P Feener
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May 8, 2018·Orphanet Journal of Rare Diseases·Emel Aygören-PürsünMarcus Maurer
Jun 20, 2018·Journal of Thrombosis and Haemostasis : JTH·S De MaatC Maas
Jul 26, 2018·The New England Journal of Medicine·Emel Aygören-PürsünMarco Cicardi
Oct 20, 2018·Clinical and Translational Allergy·Andrea ZanichelliUNKNOWN IOS Study Group
Nov 28, 2018·JAMA : the Journal of the American Medical Association·Aleena BanerjiUNKNOWN HELP Investigators

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