Hypoplastic left heart syndrome

Radiographics : a Review Publication of the Radiological Society of North America, Inc
D M BardoR P Saneto

Abstract

Hypoplastic left heart syndrome (HLHS) is a complex combination of cardiac malformations that probably results from multiple developmental errors in the early stages of cardiogenesis and that, if left untreated, invariably proves fatal. A variety of chest radiographic findings are seen in patients with HLHS, including an enlarged cardiac silhouette (notably a prominent right atrium), pulmonary venous hypertension, an atrial septal defect, and valvular stenosis or atresia. The recent evolution of palliative surgical procedures (modified Norwood procedure, bidirectional cavopulmonary shunt, modified Fontan procedure, aortic valvuloplasty, heart transplantation) has increased the survival rate in children with HLHS. Echocardiography allows accurate assessment of the size and location of the ductus arteriosus, the hemodynamics of the aortic root, the patency and size of the foramen ovale or atrial septal defect, and the presence of a ventricular septal defect to help determine whether surgical intervention is appropriate and, if so, to facilitate planning. Pediatric radiologists now view radiologic images obtained in patients with HLHS before surgical intervention and at important intervals during treatment. Familiarity with the ma...Continue Reading

References

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Citations

May 16, 2007·Pediatric Radiology·Carlos MarinJuan I Zabala
Jan 29, 2010·Pediatric Radiology·Jonathan R DillmanRamiro J Hernandez
Jun 1, 2007·Seminars in Interventional Radiology·Thomas KauKlaus Armin Hausegger
Aug 17, 2010·Journal of Thoracic Imaging·Marilyn J Siegel
Apr 1, 2008·Radiology·Ana Maria GacaGeorge S Bisset
Nov 23, 2006·Intensive Care Medicine·Sylvie Di FilippoRicardo Muñoz
Jul 9, 2014·Insights Into Imaging·Mohammed M KhadirAbhishek Chaturvedi
Jan 25, 2013·Computer Methods in Biomechanics and Biomedical Engineering·Chiara CorsiniModeling of Congenital Hearts Alliance (MOCHA) Investigators
Jun 30, 2007·The Journal of Thoracic and Cardiovascular Surgery·André M IlbawiRobert H Anderson
Jan 25, 2013·International Journal for Numerical Methods in Biomedical Engineering·Jinli DingFeng Wang
Aug 17, 2018·Journal of Clinical Ultrasound : JCU·Manisha Kumar, Priyam
Jun 13, 2020·Journal of Clinical Ultrasound : JCU·Hai-Qin LiaoQuan-Liang Shang
Oct 15, 2013·Heart·Massimiliano CantinottiIsabella Spadoni
Aug 30, 2020·Seminars in Roentgenology·Anna ShmuklerLinda B Haramati

Related Concepts

Coronary Circulation
2D Echocardiography
Magnetization Transfer Contrast Imaging
Radiography, Thoracic
Fetal Ultrasonography
Coronary Angiography
Hypoplastic Left Heart Syndrome

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