Immunoglobulin G4-associated cholangitis mimicking cholangiocarcinoma in a young boy

Journal of Postgraduate Medicine
R K MiglaniA K V Kumar

Abstract

Autoimmune pancreatitis is a rare form of chronic pancreatitis, which commonly mimics pancreatic carcinoma. Immunoglobulin G4-associated cholangitis (IAC) is a rare type of autoimmune pancreatitis associated with bile duct involvement, which can present with or without pancreatic involvement. Usually, the bile duct involvement is in the form of multiple intra-and extra-hepatic strictures mimicking primary sclerosing cholangitis. Rarely, there can be an isolated stricture which mimics cholangiocarcinoma. Differentiating these from cholangiocarcinoma, though extremely difficult, is of critical importance since it can be treated without surgical intervention. Most cases with rare presentation mimicking cholangiocarcinoma have been reported in elderly patients. We present one such rare presentation of autoimmune pancreatitis in a young 13-year-old patient in whom hepaticojejunostomy was done for a hilar stricture, which later turned out to be related to IAC. To our knowledge this is the first reported case of its kind from India.

References

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Citations

Oct 5, 2012·Journal of Gastroenterology and Hepatology·Jun LiYuechun Shen
Oct 1, 2011·Journal of Medical Case Reports·Alexandra ShinginaBaljinder Salh
Apr 23, 2013·Digestive and Liver Disease : Official Journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver·Yazid J ResheqStefan Lüth
Jun 16, 2011·Hepatology : Official Journal of the American Association for the Study of Liver Diseases·Abdul M OseiniLewis R Roberts
Mar 26, 2016·Pediatric Rheumatology Online Journal·Faiz KarimJan van Laar
Feb 20, 2018·Experimental and Therapeutic Medicine·Can ChenShenxian Qian

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