Immunoglobulin g4 non-related sclerosing disease with intracardiac mass mimicking mitral stenosis: case report

Journal of Korean Medical Science
Ji-won HwangDuk-Kyung Kim

Abstract

The cardiovascular system may be one of the target organs of both immunoglobulin G4 related and non-related systemic multifocal fibrosclerosis. We present a case of IgG4 non-related systemic multifocal fibrosclerosis mimicking mitral stenosis on echocardiography. For a more detailed differential diagnosis, we used multimodal imaging techniques. After surgical biopsy around the abdominal aortic area in the retroperitoneum, histological examination revealed IgG4 non-related systemic multifocal fibrosclerosis. We describe the multimodal imaging used to diagnose IgG4 non-related systemic multifocal fibrosclerosis and a positive response to steroid treatment. There have been no previous case reports of IgG4 non-related systemic multifocal fibrosclerosis with intracardiac involvement. Here, we report a case of IgG4 non-related systemic multifocal fibrosclerosis mimicking mitral stenosis.

References

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Citations

Feb 25, 2014·Clinical Rheumatology·Christian LöfflerRaoul Bergner
Oct 7, 2014·Cardiovascular Pathology : the Official Journal of the Society for Cardiovascular Pathology·Joseph J MaleszewskiMarc K Halushka
Sep 2, 2016·Internal Medicine·Yosuke KunishitaHideaki Nakajima
Feb 14, 2018·Annals of the Rheumatic Diseases·Benedict K TiongErnest Brahn

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Methods Mentioned

BETA
biopsy
electrophoresis
ESR

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