Infant pulmonary function testing in chronic pneumonitis of infancy due to surfactant protein C mutation

Pediatric Pulmonology
Avigdor HevroniChaim Springer

Abstract

Pulmonary function testing is a vital tool in evaluation and management of adult ILD patients and is rarely overlooked during workup. However, there is paucity of data regarding its usefulness in management of infants with suspected interstitial lung disease. In this paper, we present the contribution of infant pulmonary function testing (iPFT) to the management of two infants with biopsy confirmed chronic pneumonitis of infancy due to surfactant protein C mutation. We have productively and safely used serial iPFT for decision making both during diagnosis and follow-up of these infants.

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References

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Aug 3, 2013·American Journal of Respiratory and Critical Care Medicine·Geoffrey KurlandUNKNOWN American Thoracic Society Committee on Childhood Interstitial Lung Disease (chILD) and the chILD Research Network
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Apr 23, 2014·Current Opinion in Pediatrics·Christin S Kuo, Lisa R Young

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Citations

Jul 1, 2016·Pediatric Pulmonology·Melissa Kaori Silva LitaoLokesh Guglani
Jul 13, 2018·European Respiratory Review : an Official Journal of the European Respiratory Society·Dymph KlayColine H M van Moorsel
Jul 24, 2020·European Respiratory Review : an Official Journal of the European Respiratory Society·Astrid Madsen RingFrederik Buchvald

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