PMID: 590281Nov 4, 1977

Intelligence level of patients with the Duchenne type of progressive muscular dystrophy (pmd-d)

European Journal of Pediatrics
M Florek, S Karolak

Abstract

The I.Q. of 129 patients with PMD-D and 27 patients suffering from Werdnig-Hoffmann disease were estimated. Among the patients with PMD-D there was one group without any complicating factors and 3 other groups with additional factors that might influence the intelligence level. Comparing mean values and distribution of I.Q. for all these groups, one can conclude that, besides additional unfavourable pathological and environmental factors in all cases, PMD-D itself causes a small decrease of the I.Q. by about 1 SD. The frequent changes of the EEG record in these patients could reflect involvement of the CNS by the pathological process.

References

Oct 1, 1971·Journal of the Neurological Sciences·A KozickaR Wasilewski
Mar 1, 1968·Journal of the Neurological Sciences·I Hausmanowa-PetrusewiczE Sawicka
Dec 1, 1968·Developmental Medicine and Child Neurology·H J CohenL T Taft
Apr 1, 1969·Archives of Disease in Childhood·E J ProsserM W Thompson
Oct 1, 1967·Developmental Medicine and Child Neurology·H Zellweger, J W Hanson
Aug 1, 1960·American Journal of Diseases of Children·J E ALLEN, D W RODGIN
Jun 1, 1965·Archives of Disease in Childhood·V Dubowitz

Citations

Jan 1, 1987·European Archives of Psychiatry and Neurological Sciences·T Glaub, F Mechler
Jan 1, 1997·European Journal of Paediatric Neurology : EJPN : Official Journal of the European Paediatric Neurology Society·F GoodwinV Dubowitz
Oct 1, 1985·Journal of Clinical and Experimental Neuropsychology·N D SolleeM J Bresnan
May 13, 2017·Cold Spring Harbor Perspectives in Medicine·C'iana CooperHenriette van Praag
Mar 18, 2006·Muscle & Nerve·Maria Grazia D'Angelo, N Bresolin
Feb 9, 2002·Brain : a Journal of Neurology·J L AndersonJ W Morley
Jun 1, 1990·Developmental Medicine and Child Neurology·R A SmithP S Harper
Oct 1, 1981·Developmental Medicine and Child Neurology·D Leibowitz, V Dubowitz

Related Concepts

Teens
Clinically Isolated Syndrome, CNS Demyelinating
Electroencephalogram
Intelligence
Mental Tests
Motor Neurons
Neurogenic Muscular Atrophy
Muscular Dystrophy
Nerve Degeneration

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