Intra-utero diagnosis of anomalous right ventricular muscle bundles in association with a ventricular septal defect: a case report

Pediatric Cardiology
J LeandroJ Smallhorn

Abstract

The morphology and natural history of anomalous right ventricular muscle bundles (ARVMB) have been described in a number of postnatal studies. Whether this is a congenital or acquired cardiac lesion remains obscure. A fetal echocardiogram performed in a 32-week gestation mother showed a large ventricular septal defect and anomalous right ventricular muscle bundles, which were easily appreciated at the ostium-infundibular level. The diagnosis was confirmed postnatally and at 6 months of age the child underwent surgical repair. This report documents the presence of ARVMB in a fetus, at a time when hemodynamics cannot explain the development of right ventricular muscle bundles. It suggests that at least, the morphologic substrate for this disease is congenital.

References

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May 1, 1969·British Heart Journal·G E GaleJ B Barlow
Jul 1, 1984·Pediatric Cardiology·A RestivoS P Allwork
Apr 1, 1982·The American Journal of Cardiology·C J ByrumA Rosenthal
Apr 1, 1961·The Surgical Clinics of North America·M A ENGLEH J STEWART

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Citations

Apr 6, 2004·Ultrasound in Obstetrics & Gynecology : the Official Journal of the International Society of Ultrasound in Obstetrics and Gynecology·S BeckerG Mielke

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