[Juvenile dermatomyositis: A series of 22 cases].

Annales de dermatologie et de vénéréologie
C Moegle, D Lipsker

Abstract

To report on the characteristics of juvenile dermatomyositis (JDM). This was a retrospective, descriptive, cross-sectional, non-interventional, multicenter study conducted in Alsace between 2000 and 2015. The patients, aged 0 to 16years, had JDM according to both the Bohan and Peter and the EULAR/ACR criteria. A total of 17 girls and 5 boys were included with a median age at disease onset of 7,8years (Q1-Q3: 4.4-12.9). Median duration of JDM and median patient follow-up were 2.8years and 6.2years, respectively. The most common skin symptoms were papules or Gottron's sign (86 %), nail lesions (82 %), erythema of the face (77 %) and eyelids (59 %), photosensitivity (59 %), and calcinosis (27 %). One patient presented papules with a depressed and porcelain-white center ("Degos-like" lesions). One patient had algodystrophy. Two patients were clinically amyopathic. One girl had intestinal vasculitis. Respiratory function tests were abnormal in 27 % of cases. Median treatment duration was 42 months (Q1-Q3: 19-63). Three patients had a monocyclic form, 12 had a polycyclic form, and 7 had chronic disease. The frequency of cutaneous and musculoskeletal signs is comparable to that of other large cohorts of JDM. "Degos-like" lesions and a...Continue Reading

References

Feb 20, 1975·The New England Journal of Medicine·A Bohan, J B Peter
Feb 13, 1975·The New England Journal of Medicine·A Bohan, J B Peter
Feb 17, 1972·The New England Journal of Medicine·J N Whitaker, W K Engel
Aug 1, 1995·British Journal of Rheumatology·D P SymmonsS M Davis
Aug 1, 1994·The British Journal of Dermatology·W K CheongJ L Hawk
Feb 1, 1997·Journal of the American Academy of Dermatology·H TsaoH A Haynes
Jun 26, 2001·Journal of the American Academy of Dermatology·T M PeloroE D Newman
Nov 27, 2001·Journal of Clinical Immunology·C Cunningham-Rundles
Sep 27, 2003·Lancet·Marinos C Dalakas, Reinhard Hohlfeld
Apr 30, 2004·Clinical and Experimental Dermatology·Z ShiraniJ L Jorizzo
May 22, 2004·Journal of the American Academy of Dermatology·Whitney A HighMelissa I Costner
Jan 1, 2008·Archives de pédiatrie : organe officiel de la Sociéte française de pédiatrie·S Gissinger-PrévotB Chabrol
Jan 19, 2008·Journal of Clinical Immunology·Cristina M A JacobRenato C Monteiro
Oct 16, 2009·Journal of Medical Case Reports·Kartini F Rahim, Robert S Dawe
Aug 31, 2010·Rheumatology·Lisa G RiderUNKNOWN Childhood Myositis Heterogeneity Collaborative Study Group
Jun 17, 2011·The Journal of Rheumatology·Brigitte Bader-MeunierUNKNOWN Club Rhumatismes et Inflammation
Nov 3, 2011·Scandinavian Journal of Rheumatology·P MathiesenS Nielsen
May 3, 2013·Annals of the Rheumatic Diseases·Clara MalattiaAlberto Martini
May 10, 2013·Arthritis and Rheumatism·Mona ShahUNKNOWN Childhood Myositis Heterogeneity Collaborative Study Group
Aug 29, 2013·Arthritis Care & Research·Angela Byun RobinsonUNKNOWN Juvenile Myositis CARRA Subgroup, for the CARRA Registry Investigators
Oct 30, 2013·International Journal of Rheumatic Diseases·Peter J GowdieJonathan D Akikusa
May 27, 2014·La Revue de médecine interne·G PouesselA Deschildre
Jul 30, 2014·Rheumatology·Alain MeyerJean Sibilia
Aug 20, 2014·Journal of Clinical Neuromuscular Disease·Thy P NguyenKazim Sheikh
Nov 26, 2015·Archives de pédiatrie : organe officiel de la Sociéte française de pédiatrie·M GuarellaA Belot
Dec 10, 2015·Lancet·Nicolino RupertoUNKNOWN Paediatric Rheumatology International Trials Organisation (PRINTO)
Mar 24, 2016·Archives of Disease in Childhood·Hashem Abu-Arafeh, Ishaq Abu-Arafeh
Apr 19, 2016·The British Journal of Dermatology·E HurlimanM Hordinsky
Jun 21, 2016·Journal of Internal Medicine·I E LundbergM Bottai
Aug 16, 2016·Annals of the Rheumatic Diseases·Felicitas Bellutti EndersAnnet van Royen-Kerkhof
Nov 3, 2016·The Journal of Rheumatology·Adam M HuberUNKNOWN Juvenile Dermatomyositis Research Committee of the Childhood Arthritis and Rheumatology Research Alliance
Apr 14, 2017·Pediatric Rheumatology Online Journal·Rabheh Abdul-AzizCharles H Spencer
May 10, 2017·Journal of the Neurological Sciences·Joerg-Patrick Stübgen
May 28, 2017·Paediatric Drugs·Charalampia Papadopoulou, Lucy R Wedderburn
Jul 8, 2017·Rheumatology International·Sulaiman M Al-MayoufAbdullah Alsonbul

❮ Previous
Next ❯

Related Concepts

Trending Feeds

COVID-19

Coronaviruses encompass a large family of viruses that cause the common cold as well as more serious diseases, such as the ongoing outbreak of coronavirus disease 2019 (COVID-19; formally known as 2019-nCoV). Coronaviruses can spread from animals to humans; symptoms include fever, cough, shortness of breath, and breathing difficulties; in more severe cases, infection can lead to death. This feed covers recent research on COVID-19.

Blastomycosis

Blastomycosis fungal infections spread through inhaling Blastomyces dermatitidis spores. Discover the latest research on blastomycosis fungal infections here.

Nuclear Pore Complex in ALS/FTD

Alterations in nucleocytoplasmic transport, controlled by the nuclear pore complex, may be involved in the pathomechanism underlying multiple neurodegenerative diseases including Amyotrophic Lateral Sclerosis and Frontotemporal Dementia. Here is the latest research on the nuclear pore complex in ALS and FTD.

Applications of Molecular Barcoding

The concept of molecular barcoding is that each original DNA or RNA molecule is attached to a unique sequence barcode. Sequence reads having different barcodes represent different original molecules, while sequence reads having the same barcode are results of PCR duplication from one original molecule. Discover the latest research on molecular barcoding here.

Chronic Fatigue Syndrome

Chronic fatigue syndrome is a disease characterized by unexplained disabling fatigue; the pathology of which is incompletely understood. Discover the latest research on chronic fatigue syndrome here.

Evolution of Pluripotency

Pluripotency refers to the ability of a cell to develop into three primary germ cell layers of the embryo. This feed focuses on the mechanisms that underlie the evolution of pluripotency. Here is the latest research.

Position Effect Variegation

Position Effect Variagation occurs when a gene is inactivated due to its positioning near heterochromatic regions within a chromosome. Discover the latest research on Position Effect Variagation here.

STING Receptor Agonists

Stimulator of IFN genes (STING) are a group of transmembrane proteins that are involved in the induction of type I interferon that is important in the innate immune response. The stimulation of STING has been an active area of research in the treatment of cancer and infectious diseases. Here is the latest research on STING receptor agonists.

Microbicide

Microbicides are products that can be applied to vaginal or rectal mucosal surfaces with the goal of preventing, or at least significantly reducing, the transmission of sexually transmitted infections. Here is the latest research on microbicides.

Related Papers

Journal of Pediatric Gastroenterology and Nutrition
Caroline BesnardBrigitte Bader-Meunier
Journal of Pediatric Gastroenterology and Nutrition
Caroline BesnardBrigitte Bader-Meunier
© 2022 Meta ULC. All rights reserved