PMID: 12760437May 23, 2003Paper

Left-sided facial nevus with contralateral leptomeningeal angiomatosis in a child with Sturge-Weber syndrome: case report

Journal of Child Neurology
Peter Widdess-Walsh, Neil Roy Friedman

Abstract

Sturge-Weber syndrome is characterized by a facial vascular nevus associated with an ipsilateral leptomeningeal angioma. Variants of this classical presentation have been described in the literature, some of which have prognostic significance. We report a magnetic resonance imaging (MRI)-confirmed variant of a leptomeningeal angioma contralateral to the facial nevus. We describe one patient with Sturge-Weber syndrome who presented with a left-sided facial nevus, left eye glaucoma, episodes of left-sided weakness, and right-sided leptomeningeal angiomatosis by gadolinium-enhanced brain MRI. The literature regarding variants of Sturge-Weber syndrome and their prognosis is reviewed. The prognosis for this variant is likely similar to Sturge-Weber syndrome with an ipsilateral leptomeningeal angioma.

References

Aug 1, 1995·Neuropediatrics·I Pascual-CastroviejoJ Coya
Apr 30, 1998·Neuroradiology·N J FischbeinB O Berg
Jul 29, 2000·Pediatric Neurology·A AydinE Dirik
Oct 6, 2000·American Journal of Ophthalmology·A AmirikiaT G Murray

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Citations

Mar 12, 2010·La Presse médicale·Annabel Maruani
Aug 7, 2004·Seminars in Cutaneous Medicine and Surgery·Eulalia Baselga

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