Abstract
Left ventricular noncompaction is a rare cardiomyopathy characterized by a thin, compacted epicardial layer and a noncompacted endocardial layer, with trabeculations and recesses that communicate with the left ventricular cavity. In the advanced stage of the disease, the classical triad of heart failure, ventricular arrhythmia, and systemic embolization is common. Segments involved are the apex and mid inferior and lateral walls. The right ventricular apex may be affected as well. A 29-year-old Caucasian male was hospitalized with dyspnea and fatigue at minimal exertion during the last months before admission. He also described a history of edema of the legs and abdominal pain in the last weeks. Physical examination revealed dyspnea, pulmonary rales, cardiomegaly, hepatomegaly, and splenomegaly. Electrocardiography showed sinus rhythm with nonspecific repolarization changes. Twenty-four-hour Holter monitoring identified ventricular tachycardia episodes with right bundle branch block morphology. Transthoracic echocardiography at admission revealed dilated left ventricle with trabeculations located predominantly at the apex but also in the apical and mid portion of lateral and inferior wall; end-systolic ratio of noncompacted to ...Continue Reading
References
Aug 1, 1990·Circulation·T K ChinR Mohrmann
Nov 17, 2001·Heart·R JenniP A Kaufmann
Jan 9, 2004·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·Claudia Stöllberger, Josef Finsterer
Jul 5, 2005·Journal of the American College of Cardiology·Steffen E PetersenStefan Neubauer
Mar 29, 2006·Circulation·Barry J MaronUNKNOWN Council on Epidemiology and Prevention
Oct 6, 2007·European Heart Journal·Perry ElliottAndre Keren
Sep 26, 2008·European Journal of Heart Failure·Bas M van DalenMarcel L Geleijnse
Nov 6, 2009·European Journal of Echocardiography : the Journal of the Working Group on Echocardiography of the European Society of Cardiology·Dewi E ThomasNavroz D Masani
Jan 22, 2010·European Heart Journal·Alexis JacquierGuy Moulin
Aug 4, 2011·Europace : European Pacing, Arrhythmias, and Cardiac Electrophysiology : Journal of the Working Groups on Cardiac Pacing, Arrhythmias, and Cardiac Cellular Electrophysiology of the European Society of Cardiology·Michael J AckermanUNKNOWN European Heart Rhythm Association (EHRA)
Nov 1, 2011·The American Journal of Cardiology·Matthias GreutmannErwin N Oechslin
Jan 6, 2012·European Journal of Heart Failure·Markus NiemannFrank Weidemann
Jul 10, 2012·European Radiology·Matthias GrothoffMatthias Gutberlet
Aug 14, 2012·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·Catherine GebhardFelix C Tanner
Jun 26, 2013·European Heart Journal Cardiovascular Imaging·Ferande PetersMohammed R Essop
Jan 7, 2015·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·Roberto M LangJens-Uwe Voigt
Sep 1, 2015·European Heart Journal·Silvia G PrioriDirk J Van Veldhuisen
Feb 18, 2016·Cardiology Research and Practice·Courtney E Bennett, Ronald Freudenberger
Feb 16, 2018·Journal of the American College of Cardiology·Jaap I van WaningDanielle Majoor-Krakauer
Feb 16, 2018·Journal of the American College of Cardiology·Erwin Oechslin, Rolf Jenni
Jan 22, 2020·Circulation. Cardiovascular Imaging·Nay AungSteffen E Petersen