Levoatrial cardinal vein with normal left ventricle: A forgotten cause of pulmonary arterial hypertension

The Indian Journal of Radiology & Imaging
Onkar B AutiVimal Raj

Abstract

Levoatrial cardinal vein (LACV) is anomalous connection between left atrium or pulmonary veins and systemic veins such as innominate vein or superior vena cava. This persistence of splanchnic circulation occurs when there is left-sided obstructive cardiac lesions such as hypoplastic left heart or mitral atresia. In this report we present three cases of LACV with well-developed left heart, without any obstructive lesions. All our cases presented with pulmonary arterial hypertension (PAH) and had associated intracardiac shunt such as ventricular/atrial septal defect and supracardiac partial anomalous pulmonary venous connection. Apart from the above shunts, LACV contributed to PAH in these cases. It is important to detect and report LACV as this may require surgical correction along with other defects. If LACV goes undetected during imaging workup, it may cause persistent PAH postoperatively.

References

Oct 1, 1995·Journal of the American College of Cardiology·H S BernsteinN H Silverman
Feb 13, 1999·Pediatric Cardiology·K FujiwaraH Suzuki
Jan 24, 2006·The Annals of Thoracic Surgery·Toshio KanedaNobuyuki Mori
Oct 7, 2011·Annals of Pediatric Cardiology·Ender OdemisAli Riza Karaci
Apr 18, 2013·European Heart Journal Cardiovascular Imaging·Paolo CilibertiAlessandro Giardini

Citations

Jan 4, 2020·Circulation. Heart Failure·Suneet N PurohitNatasha L Altman
Jan 8, 2021·World Journal for Pediatric & Congenital Heart Surgery·Kartik PatelTrushar Gajjar

Related Concepts

Structure of Brachiocephalic Vein
Diagnostic Imaging
Heart
Pulmonary Hypertension
Obstruction
Pulmonary Veins
Splanchnic Circulation
Veins
Hypoplastic Left Heart Syndrome
Left Atrial Structure

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