Liver transplantation for a hilar inflammatory myofibroblastic tumor

Pediatric Transplantation
D DasguptaM D Stringer

Abstract

A 7-yr-old boy presented with obstructive jaundice secondary to an inflammatory myofibroblastic tumor centered on the hepatic hilum and extending into the liver. The tumor was further complicated by portal vein phlebitis and occlusion. Attempted resection of the tumor with portal vein reconstruction and bilioenteric drainage was unsuccessful and he required urgent orthotopic liver transplantation. In contrast to more peripheral inflammatory myofibroblastic tumors in the liver, hilar lesions are locally aggressive, causing occlusive portal phlebitis and biliary obstruction. Successful management may include the need for liver transplantation.

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Citations

Oct 22, 2009·AJR. American Journal of Roentgenology·Su Jin KimKyung Mo Yeon
Sep 10, 2008·Journal of Pediatric Surgery·Paul NeedhamMark D Stringer
Nov 15, 2006·Journal of Pediatric Surgery·Richard J England, Mark D Stringer
Jun 12, 2012·Renal Failure·Yong-Heng HuangYun-Le Wan
Feb 24, 2007·Annals of the Royal College of Surgeons of England·Mark D Stringer
Oct 18, 2019·ACG Case Reports Journal·Aravind ThavamaniKadakkal Radhakrishnan
Aug 27, 2013·Journal of Pediatric Gastroenterology and Nutrition·Sudhan NagarajanManuel I Rodriguez-Davalos

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