PMID: 11906647Mar 22, 2002Paper

Living-related liver transplantation for biliary atresia associated with polysplenia syndrome

Pediatric Transplantation
Toshimichi HasegawaAkira Okada

Abstract

This report describes a 1-yr-old boy with biliary atresia (BA) and polysplenia syndrome (PS) who underwent successful living-related liver transplantation (LTx). At the time of initial hepatic portoenterostomy, he was noticed to have a preduodenal portal vein (PV), non-rotation of the intestine, and polysplenia. Because he did not achieve good bile excretion, he underwent a living-related LTx (using a left lateral segment from his mother) at the age of 14 months. Evaluation of the vascular anatomy was made by angiography, magnetic resonance imaging (MRI), computerized tomography (CT), and Doppler ultrasound. The PV was stenotic from the confluence of the superior mesenteric vein (SMV) and splenic vein (SpV) to the hepatic hilum. The retrohepatic inferior vena cava (IVC) was deficient cranially to the renal vein and was connected to the azygous vein. The supra-hepatic IVC was detected below the diaphragm and was connected to three hepatic veins. The common hepatic artery (HA) originated from the superior mesenteric artery. At LTx, the PV was dissected to the level of confluence of the SMV and the SpV, from which the venous graft was interposed using the donor's ovarian vein. Three hepatic veins were plastied into one orifice, wh...Continue Reading

References

May 1, 1991·Journal of Pediatric Surgery·F M KarrerJ R Lilly
May 1, 1991·Journal of Pediatric Surgery·D FalchettiJ B Otte
Mar 1, 1988·Transplantation·S C RaynorB W Shaw
Oct 1, 1974·Journal of Pediatric Surgery·J R Lilly, T E Starzl
Feb 1, 1995·The British Journal of Surgery·C J WatsonR Y Calne
Mar 1, 1995·Journal of Pediatric Surgery·J VazquezJ A Tovar
Jan 1, 1997·Journal of Pediatric Surgery·K NakadaN Yamate
Jan 9, 1999·Pediatric Surgery International·P MatteiP M Colombani
Nov 7, 1999·Transplantation·M A MaggardR W Busuttil
Dec 11, 1999·Journal of Pediatric Surgery·H TananoA Okada

❮ Previous
Next ❯

Citations

Nov 19, 2009·Clinical Transplantation·Settimo CarusoBruno Gridelli
Feb 17, 2007·Clinical Transplantation·Ender DulunduMasatoshi Makuuchi
Feb 18, 2009·World Journal of Gastroenterology : WJG·Settimo CarusoBruno Gridelli
Dec 17, 2009·Pediatrics International : Official Journal of the Japan Pediatric Society·Ming-Chun YangHuey-Ling Chen
Feb 4, 2005·Liver Transplantation : Official Publication of the American Association for the Study of Liver Diseases and the International Liver Transplantation Society·Julie K HeimbachCharles B Rosen
Aug 18, 2021·Annals of Hepato-biliary-pancreatic Surgery·Jung-Man NamgoongYong Jae Kwon

❮ Previous
Next ❯

Related Concepts

Trending Feeds

COVID-19

Coronaviruses encompass a large family of viruses that cause the common cold as well as more serious diseases, such as the ongoing outbreak of coronavirus disease 2019 (COVID-19; formally known as 2019-nCoV). Coronaviruses can spread from animals to humans; symptoms include fever, cough, shortness of breath, and breathing difficulties; in more severe cases, infection can lead to death. This feed covers recent research on COVID-19.

Blastomycosis

Blastomycosis fungal infections spread through inhaling Blastomyces dermatitidis spores. Discover the latest research on blastomycosis fungal infections here.

Nuclear Pore Complex in ALS/FTD

Alterations in nucleocytoplasmic transport, controlled by the nuclear pore complex, may be involved in the pathomechanism underlying multiple neurodegenerative diseases including Amyotrophic Lateral Sclerosis and Frontotemporal Dementia. Here is the latest research on the nuclear pore complex in ALS and FTD.

Applications of Molecular Barcoding

The concept of molecular barcoding is that each original DNA or RNA molecule is attached to a unique sequence barcode. Sequence reads having different barcodes represent different original molecules, while sequence reads having the same barcode are results of PCR duplication from one original molecule. Discover the latest research on molecular barcoding here.

Chronic Fatigue Syndrome

Chronic fatigue syndrome is a disease characterized by unexplained disabling fatigue; the pathology of which is incompletely understood. Discover the latest research on chronic fatigue syndrome here.

Evolution of Pluripotency

Pluripotency refers to the ability of a cell to develop into three primary germ cell layers of the embryo. This feed focuses on the mechanisms that underlie the evolution of pluripotency. Here is the latest research.

Position Effect Variegation

Position Effect Variagation occurs when a gene is inactivated due to its positioning near heterochromatic regions within a chromosome. Discover the latest research on Position Effect Variagation here.

STING Receptor Agonists

Stimulator of IFN genes (STING) are a group of transmembrane proteins that are involved in the induction of type I interferon that is important in the innate immune response. The stimulation of STING has been an active area of research in the treatment of cancer and infectious diseases. Here is the latest research on STING receptor agonists.

Microbicide

Microbicides are products that can be applied to vaginal or rectal mucosal surfaces with the goal of preventing, or at least significantly reducing, the transmission of sexually transmitted infections. Here is the latest research on microbicides.